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Abstract

Non immune hydrops fetalis is defined as the excessive accumulation of fluid in two or more compartments of the fetus in the absence of any maternal-fetal blood incompatibility. The clinical presentations include ascites, scalp edema, pleural or pericardial effusions and polyhydramnios. Perinatal mortality in this severe clinical condition is high, between 50-98%. Prematurity is an important risk factor for mortality. Despite many advances in diagnosis, therapy and ventilation management during the last decade in neonatal intensive care units, the mortality rate has not changed very much for hydropic infants. This is the report of the management of two premature infants born severely hydropic. The first infant had tachyarrhythmia, the second infant had Noonan syndrome. Both infants had a good prognosis.

Keywords

• Non immune hydrops fetalis, Fetal tachyarrhythmia, Noonan syndrome

Non immun hidrops fetalis: İyi prognozlu iki prematüre olgu

Abstract

Non immun hidrops fetalis anne ve bebek arasında kan uyuşmazlığı olmaksızın fetüsde iki veya daha fazla vücut boşluğunda fazla sıvı birikmesi olarak tanımlanır. Asit, saçlı deride ödem, plevral ve perikardiyal efüzyon ve polihidramnios klinik tabloyu oluşturur. Bu ağır klinik tabloda perinatal mortalite %50-98 arasında yüksektir. Prematüre doğum mortalite için önemli bir risk faktörüdür. Yenidoğan yoğun bakım ünitelerinde son on yılda tanı, tedavi ve ventilasyon uygulamalarındaki gelişmelere rağmen, hidropik bebeklerde mortalite oranları fazla değişmemiştir. Bu yazıda hidropik doğan iki prematüre bebeğin takibi sunulmuştur. Birinci olguda fetal taşiaritmiye, ikinci olguda Noonan sendromuna bağlı non immun hidrops fetalis gelişmiştir. İki vakada da prognoz iyi olmuştur.

Keywords

• Non immun hidrops fetalis, Fetal taşiaritmi, Noonan sendromu

References

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