Ultrasound and MRI features of lipomatosis of the median nerve: A case study

Abstract

We present a case of a 10 year-old girl with slowly enlarging,

painless mass at the volar aspect of her left hand. The lesion

had been present since infancy. Diagnosis was lipomatosis of

the median nerve which is a very rare, benign tumor involving

peripheral nerves. Magnetic resonance imaging (MRI) and

ultrasound (US) features of this lesion are discussed.

Keywords

• Median nerve lipomatosis,Fibrolipomatous hamartoma,Congenital tumor,Peripheral nerve

Median sinir lipomatozisinin ultrason ve MR görüntüleme özellikleri

Abstract

Bu vaka bildiriminde, sol el volar yüzde, infant döneminden beri

olan, yavaş büyüyen, ağrısız şişlik şikayeti olan 10 yaşında bir

kız çocuğu sunulmaktadır. Tanı, periferik sinirleri tutan çok nadir,

benign bir tümör olan median sinirin lipomatozisi idi. Yazıda

median sinir lipomatozisinin magnetik rezonans görüntü (MRG)

ve ultrason (US) özellikleri tartışıldı.

Keywords

• Median sinir lipomatozisi,Fibrolipomatöz hamartom,Konjenital tümör,Periferik sinir

References

1. 1. Nilsson J, Sandberg K, Dahlin LB, et al. Fibrolipomatous hamartoma in the median nerve in the arm – an unusual location but with MR imaging characteristics: a case report. J Brachial Plex Peripher Nerve Inj 2010;5:1. doi: 10.1186/1749-7221-5-1
2. 2. Mason M. Presentation of cases. In: Proceedings of the American Society for Surgery of the Hand, 1953. J Bone Joint Surg Am 1953; 35A:273-5.
3. 3. Johnson RJ, Bonfigilio M. Lipofibromatous hamartoma of the median nerve. J Bone Joint Surg 1969;51:984-90.
4. 4. Christopher D, Unni K, Mertens F. Adipocytic tumors. In: Fletcher CDM, Unni K Mertens F, editors. WHO Classification of tumors. Pathology and genetics: tumors of soft tissue and bone. IARC 2002; 19-46.
5. 5. Julien TP. Lipofibromatous hamartoma: A review article. OHJMS 2009;11:87-90.
6. 6. Kransdorf M, Murphey M. Lipomatous tumors. Imaging of soft tissue tumors. Philadelphia: Pa: Saunders, 1997; 57-101.
7. 7. Louaste J, Zejjari H, Chkoura M, Houmadi A, Rachid K: Carpal tunnel syndrome due to fibrolipomatous hamartoma of the median nerve. Hand (N Y) 2011;6:76-9. doi: 10.1007/ s11552-010-9290-8
8. 8. Guthikonda M, Rengachary SS, Balko MG, van Loveren H. Lipofibromatous hamartoma of the median nerve: Case report with magnetic resonance imaging correlation. Neurosurgery 1994;35:127-32.

9. 9. Chiang CL, Tsai MY, Chen CK. MRI diagnosis of fibrolipomatous hamartoma of the median nerve and associated macrodystrophia lipomatosa. J Chin Med Assoc 2010;73:499-502. doi: 10.1016/S1726-4901(10)70107-6.
10. 10. Silverman TA, Enzinger FM. Fibrolipomatous hamartoma of nerve: a clinicopathologic analysis of 26 cases. Am J Surg Pathol 1985;9:7-14.
11. 11. Azeemuddin M, Waheed AA, Khan N, Sayani R, Ahmed A. Fibrolipomatous hamartoma of the median nerve with macrodystrophia lipomatosa. Cureus 2018;10:e2293. doi:10.7759/cureus.2293.
12. 12. Toms AP, Anastakis D, Bleakney RR, et al. Lipofibromatous hamartoma of the upper extremity: a review of the radiologic findings for 15 patients. AJR Am J Roentgenol 2006;186:805-11. doi:10.2214/AJR.04.1717