Year 2015, Volume 28 , Issue 3, Pages 169 - 172 2015-11-28

Giant gluteal pilomatrixoma: An uncommon tumor in a rare localization
Dev gluteal pilomatriksoma: Nadir bir lokalizasyonda sıradışı bir tümör

Murat KILIÇ [1] , Meral ŞEN [2]


Pilomatrixoma is an uncommon, benign subcutaneous tumor arising from the hair follicle matrix. This tumor occurs more commonly in children than in adults, and most often originates on the head, neck or upper extremities. Gluteal region is an extremely rare site of pilomatrixoma. Multiple presentation is an unusual condition and often associated with some familial syndromes such as myotonic dystrophy, Gardner syndrome and Turner syndrome. Pilomatrixoma mostly presents as a painless, firm, slow-growing subcutaneous mass, and is usually encapsulated by connective tissue and sharply demarcated from the surrounding normal tissue. Both clinical and radiological findings are non-specific, and therefore histopathology is necessary to reach correct diagnosis. These lesions have very low risk of malignant transformation, and surgical excision with adequate margins is the treatment of choice. Herein, a rare case of gluteal pilomatrixoma with multiple presentation in the upper extremities in a young female patient was presented.
Pilomatriksoma saç folikülü matriksinden kaynaklanan nadir, benign bir cilt altı tümörüdür. Bu tümör yetişkinlere oranla çocuklarda daha sık görülür ve çoğu baş, boyun veya üst ekstremitelerden köken alır. Gluteal bölge, pilomatriksomanın çok nadir görülen bir bölgesidir. Multipl prezentasyon sık olmayan bir durumdur ve genellikle miyotonik distrofi, Gardner sendromu ve Turner sendromu gibi bazı ailesel sendromlar ile ilişkilidir. Pilomatriksoma çoğunlukla ağrısız, sert, yavaş büyüyen bir cilt altı kitlesi olarak ortaya çıkar ve genellikle bağ dokusu ile kapsüllü ve normal çevre dokudan keskin olarak sınırlanmıştır. Hem klinik ve hem de radyolojik bulgular spesifik değildir ve bu nedenle histopatoloji doğru tanıya ulaşmak için gereklidir. Bu lezyonlar çok düşük malign transformasyon riskine sahiptir ve tedavisi yeterli sınırlar ile cerrahi eksizyondur. Bu yazıda, genç bir kadın hastada, üst ekstremite multipl prezentasyon ile birlikte olan nadir bir gluteal pilomatriksoma olgusu sunuldu.
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Primary Language en
Subjects Medicine
Journal Section Case Reports
Authors

Author: Murat KILIÇ

Author: Meral ŞEN

Dates

Publication Date : November 28, 2015

Bibtex @research article { marumj3218, journal = {Marmara Medical Journal}, issn = {1019-1941}, eissn = {1309-9469}, address = {}, publisher = {Marmara University}, year = {2015}, volume = {28}, pages = {169 - 172}, doi = {10.5472/MMJcr.2803.04}, title = {Giant gluteal pilomatrixoma: An uncommon tumor in a rare localization}, key = {cite}, author = {Kılıç, Murat and Şen, Meral} }
APA Kılıç, M , Şen, M . (2015). Giant gluteal pilomatrixoma: An uncommon tumor in a rare localization . Marmara Medical Journal , 28 (3) , 169-172 . DOI: 10.5472/MMJcr.2803.04
MLA Kılıç, M , Şen, M . "Giant gluteal pilomatrixoma: An uncommon tumor in a rare localization" . Marmara Medical Journal 28 (2015 ): 169-172 <https://dergipark.org.tr/en/pub/marumj/issue/433/3218>
Chicago Kılıç, M , Şen, M . "Giant gluteal pilomatrixoma: An uncommon tumor in a rare localization". Marmara Medical Journal 28 (2015 ): 169-172
RIS TY - JOUR T1 - Giant gluteal pilomatrixoma: An uncommon tumor in a rare localization AU - Murat Kılıç , Meral Şen Y1 - 2015 PY - 2015 N1 - doi: 10.5472/MMJcr.2803.04 DO - 10.5472/MMJcr.2803.04 T2 - Marmara Medical Journal JF - Journal JO - JOR SP - 169 EP - 172 VL - 28 IS - 3 SN - 1019-1941-1309-9469 M3 - doi: 10.5472/MMJcr.2803.04 UR - https://doi.org/10.5472/MMJcr.2803.04 Y2 - 2021 ER -
EndNote %0 Marmara Medical Journal Giant gluteal pilomatrixoma: An uncommon tumor in a rare localization %A Murat Kılıç , Meral Şen %T Giant gluteal pilomatrixoma: An uncommon tumor in a rare localization %D 2015 %J Marmara Medical Journal %P 1019-1941-1309-9469 %V 28 %N 3 %R doi: 10.5472/MMJcr.2803.04 %U 10.5472/MMJcr.2803.04
ISNAD Kılıç, Murat , Şen, Meral . "Giant gluteal pilomatrixoma: An uncommon tumor in a rare localization". Marmara Medical Journal 28 / 3 (November 2015): 169-172 . https://doi.org/10.5472/MMJcr.2803.04
AMA Kılıç M , Şen M . Giant gluteal pilomatrixoma: An uncommon tumor in a rare localization. Marmara Med J. 2015; 28(3): 169-172.
Vancouver Kılıç M , Şen M . Giant gluteal pilomatrixoma: An uncommon tumor in a rare localization. Marmara Medical Journal. 2015; 28(3): 169-172.
IEEE M. Kılıç and M. Şen , "Giant gluteal pilomatrixoma: An uncommon tumor in a rare localization", Marmara Medical Journal, vol. 28, no. 3, pp. 169-172, Nov. 2015, doi:10.5472/MMJcr.2803.04