Dev gluteal pilomatriksoma: Nadir bir lokalizasyonda sıradışı bir tümör

Year 2015, Volume: 28 Issue: 3, 169 - 172, 28.11.2015

Murat Kılıç Meral Şen

https://doi.org/10.5472/MMJcr.2803.04

Abstract

Pilomatriksoma saç folikülü matriksinden kaynaklanan nadir,
benign bir cilt altı tümörüdür. Bu tümör yetişkinlere oranla
çocuklarda daha sık görülür ve çoğu baş, boyun veya üst
ekstremitelerden köken alır. Gluteal bölge, pilomatriksomanın
çok nadir görülen bir bölgesidir. Multipl prezentasyon sık olmayan
bir durumdur ve genellikle miyotonik distrofi, Gardner sendromu
ve Turner sendromu gibi bazı ailesel sendromlar ile ilişkilidir.
Pilomatriksoma çoğunlukla ağrısız, sert, yavaş büyüyen bir cilt altı
kitlesi olarak ortaya çıkar ve genellikle bağ dokusu ile kapsüllü ve normal çevre dokudan keskin olarak sınırlanmıştır. Hem klinik
ve hem de radyolojik bulgular spesifik değildir ve bu nedenle
histopatoloji doğru tanıya ulaşmak için gereklidir. Bu lezyonlar
çok düşük malign transformasyon riskine sahiptir ve tedavisi
yeterli sınırlar ile cerrahi eksizyondur. Bu yazıda, genç bir kadın
hastada, üst ekstremite multipl prezentasyon ile birlikte olan nadir
bir gluteal pilomatriksoma olgusu sunuldu.

Keywords

Diagnosis, Gluteus, Pilomatriksoma, Tedavi

Giant gluteal pilomatrixoma: An uncommon tumor in a rare localization

Abstract

Pilomatrixoma is an uncommon, benign subcutaneous tumor
arising from the hair follicle matrix. This tumor occurs more
commonly in children than in adults, and most often originates on
the head, neck or upper extremities. Gluteal region is an extremely
rare site of pilomatrixoma. Multiple presentation is an unusual
condition and often associated with some familial syndromes such
as myotonic dystrophy, Gardner syndrome and Turner syndrome.
Pilomatrixoma mostly presents as a painless, firm, slow-growing
subcutaneous mass, and is usually encapsulated by connective
tissue and sharply demarcated from the surrounding normal tissue.
Both clinical and radiological findings are non-specific, and
therefore histopathology is necessary to reach correct diagnosis.
These lesions have very low risk of malignant transformation,
and surgical excision with adequate margins is the treatment of
choice. Herein, a rare case of gluteal pilomatrixoma with multiple
presentation in the upper extremities in a young female patient was
presented.

Keywords

Diagnosis, Gluteus, Pilomatrixoma, Treatment

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