DOWN SENDROMLU BİR OLGUDA BAZAL GANGLİYON KALSİFİKASYONU

Year 2004, Volume: 5 Issue: 3, 41 - 42, 01.12.2004

Tanıl Kendirli Bahar Emine Bingöler Ercan Tutar Erdal İnce Gülhis Deda

Abstract

Sekiz yaşında, Down sendromlu, erkek hasta pnömoni ve solunum yetmezliğiyle Çocuk Yoğun Bakım Ünitesinekabul edildi. İzleminde tremor, strabismus, idrar retansiyonu ve klonus fark edildi. Bu nörolojik bulgular içinçekilen bilgisayarlı beyin tomografisinde bilateral bazal gangliyon kalsifikasyonu gösterildi. Ayrıca nörolojikbulgular kusmalarını önlemek amacıyla başlanan metoklopramide bağlandı. Hastanın bazal gangliyonkalsifikasyonunun TORCH, metabolik ve endokrin nedenlere bağlı olmadığı gösterilerek Down sendromunabağlı olduğu düşünüldü

Keywords

Down sendromu, bazal gangliyon kalsifikasyonu

A Case of Down Syndrome With Basal Ganglıa Calcification

Abstract

Eight-year-old boy with Down syndrome was accepted to The Pediatric Intensive Care Unit for pneumonia and respiratory failure. Tremor, strabismus, urinary retantion and clonus were observed during his hospitalization. Bilateral basal ganglia calcification was demonstrated by computerized tomography neurologic findings were included to be due to metoclopramid which had been begun for vomiting. Bilateral basal ganglia calcification was decided to be due to Down syndrome after excluding TORCH, metabolic and endocrin causes.

Keywords

Down syndrome, basal ganglia calcification

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