TALASEMİ HASTALARINDA ABDOMİNAL ULTRASONOGRAFİ BULGULARI

Year 2009, Volume: 10 Issue: 1, 7 - 10, 01.04.2009

Yasemin Isık Balcı Semra Demırlenk Semra Balın Özlem Özler

Abstract

AMAÇ:Bu çalışmanın amacı, Denizli Devlet Hastanesi Talasemi Merkezinde izlenen talasemi major vetalasemi intermedia hastalarının rutin abdominal ultrasonografik incelemeleri seyrinde görülenhepatosplenomegali dışındaki abdominal solid organlar ile ilgili bulgularını değerlendirmektir.GEREÇ ve YÖNTEMLER:Bu çalışmaya, 73'ü talasemi major, 5'i talasemi intermedia olmak üzere, yaşları 2ile 30 yıl arasında, 40 kız, 38 erkek hasta alınmıştır.BULGULAR:Safra kesesinde taş ve çamur (%8.9) en sık görülen bulgu idi. Aksesuar dalak 6 hastada (%7.7),karaciğerde ekojenite artışı 2 hastada (%2.6), karaciğerde hemanjiom 1 hastada(%1.3), portal ven trombozu 1hastada(%1.3) saptandı. Bir talasemi major hastasında, bilateral renal kist ve sağ renal taş ve beraberinde safrakesesinde taş görüldü.SONUÇ:Talasemi hastalarında abdominal ultrasonografik inceleme, komplikasyonların önlenmesi ve etkiliklinik izlem için düzenli aralıklar ile yapılmalıdır

Keywords

Abdominal ultrasonografi, talasemi major, talasemi intermedia

Abdominal Ultrasonographic Findings in Patients with Thalassemia

Abstract

OBJECTIVE: The aim of this study was to evaluate the type and prevalance of abdominal ultrasonographic abnormalities except hepatosplenomegaly in patients with thalassemia major and thalassemia intermedia. MATERIAL and METHODS: Seventy-eight patients; 73 thalassemia major, 5 thalassemia intermedia followed in Denizli State Hospital Thalassemia Center were included in the study. The patients' ages ranged from 2 to 30 years, with 40 females, 38 males. RESULTS: The most frequent ultrasonografic findings were cholelithiasis (8.9%), accesory spleen (7.7%), hepatic grade I-II echogenity (2,6%), hepatic hemangioma (1.3%) and portal vein thrombosis (1.3%). One case was diagnosed with polycystic kidney disease with coexisting nephrolitiasis and cholelithiasis. CONCLUSION: Abdominal ultrasonographic imaging of patients with thalassemia patients should be done regularly to prevent complications and for effective clinical observation.

Keywords

Abdominal ultrasonography, thalassemia major, thalassemia intermedia

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