Adenoid Cystic Carcinoma of Vulva: Case Report

Year 2019, Volume: 1 Issue: 2, 53 - 56, 01.12.2019

Terrab Fatima Zahrae , Rajae Ennouichi Fadoua Allouche , Zenab Alami Touria Bouhafa Khalid Hassouni

Abstract

Vulvanın adenoid kistik karsinomu: Olgu sunumu

Abstract

The adenoid cystic carcinoma (ACC) of the Bartholin’s gland (BG) is one of the most 

uncommon variant of vulvar malignancies representing only 10–15% of cases. Risk 

factors to the development of ACCBG are still unclear. The symptoms are usually 

non-specific . 

In the present study, we present a 61-year-old woman with a vulvar mass evolving 

since 4 years, without pruritus or pains, without other signs. She initially benefited of 

an excisional biopsy of the mass returning in favour of a nodular hidradenoma. The 

evolution after 1 year was marked by the recurrence of the mass, the patient had an 

ablation of the masse then a total vulvectomy and bilateral lymph node dissection 

because pathology showed ACC of Bartholin’s gland with positif surgical margins. 

She received adjuvant external beam radiation to the pelvis and on the operating 

bed. Patient’s evolution was marked by complete remission maintained after 4years 

follow-up.

Conclusion : Adenoid cystic carcinoma of vulva is an extremely rare, slowly 

progressing neoplasm mostly involving the Bartholin’s gland. The usual treatment 

includes wide excision and adjuvant radiotherapy (if required). There may be late 

local and distant recurrence.

Keywords

adenoid cystic carcinoma, bartholin's gland, surgery, radiotherapy, chemotherapy, surhical margins

References

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