An unusual reason of abdominal pain: A case of Rapunzel's syndrome and literature review

Abstract

Bezoar is defined as a mass formed as a consequence of the accumulation of indigestible foreign substances within the gastric outlet or small bowels with resultant dysfunctional gastric emptying Gastric bezoar extending into the  small or large bowel and causing a clinical condition called Rapunzel syndrome This rare pediatric condition is observed in young girls with psychiatric problems such as trichotilomania, who frequently feel an irresistable desire to pluck out, and swallow their hairs. A 12-year-old girl was admitted to our hospital with complaints of abdominal pain, growth retardation, and partial hair loss. Endoscopic examination revealed the presence of gastroduodenale trichobezoar, and her giant trichobezoar was extracted using conventional laparotomy, and anterior gastrostomy. With this case representation we reported a case with Rapunzel Syndrome in the light of literature data.

Keywords

• Unusual abdominal pain, gastroduodenal trichobezoar, trichotillomania, abdominal mass, growth retardation, laparotomy, child

An unusual reason of abdominal pain: Rapunzel syndrome case report and literature review

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References

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