Thyroid Hemiagenesis Co-occurance with Unilateral Renal Agenesis

Year 2025, Volume: 1 Issue: 1, 38 - 42, 24.01.2025

Özhan Özcan , Celil Uğurlu , İbrahim Erdim

Abstract

Thyroid Hemiagenesis (THA) is an uncommon congenital disorder characterized by the failure of one thyroid lobe with or without the isthmus to develop. This condition may arise from an abnormal descent or agenesis of the thyroid tissue. Many cases of THA remain asymptomatic and are frequently detected incidentally. This report presents a patient with multinodular goiter, concomitant left-sided thyroid, and renal agenesis. A 40-year-old male presented with a longstanding progressive thyroid enlargement, exhibiting euthyroid status. The patient reported compressive symptoms, including dysphagia, dyspnea, and hoarseness due to the goiter's size. This case report documents the first known case of concurrent THA and Unilateral Renal Agenesis (URA), underscoring the importance of thorough preoperative evaluation for congenital anomalies in THA patients. The absence of the left-sided paired organs in this patient adds to the growing body of literature on the association between these congenital abnormalities.

Keywords

Multinodular Goiter, Thyroid hemiagenesis, Unilateral Renal Agenesis

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