Giant cephalhematoma following minor head injury in a patient with Ehlers-Danlos Syndrome: A case report and literature review

Abstract

Ehlers-Danlos syndrome (EDS) is an extremely rare disease characterized by connective tissue fragility. It is characterized by laxity of ligaments, leading to joint hypermobility and hyperextensibility of the skin. The fragility of the vessels and hyper extensibility of the skin may complicate the development of large soft tissue hematomas after minor trauma, which may result in serious morbidity and mortality. We report a case of giant cephalhematoma in an 11--11-year-old boy with Ehlers-Danlos syndrome following a minor head injury. The cephalhematoma increased in size within hours and extended to involve the neck and upper chest wall, resulting in hypovolemic shock and cardiac arrest.

Keywords

• Cephalhaematoma
• Ehler-Danlos syndrome
• Head injury
• Mortality

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