Delayed diagnosis of selective immunoglobulin deficiency: A case report

Abstract

Selective immunoglobulin A deficiency (SIgAD) is the most common of all primary immunodeficiency diseases; however, the pathogenesis has not been fully understood. Although most people with SIgAD are asymptomatic, some may present with recurrent infections; such as respiratory disorders, gastrointestinal tracts disorders, and allergic disorders. Herein, we report a case with SIgAD who presented with the complaints of pruritus, dental caries and chronic sinopulmonary infections.

Keywords

• Pruritus,Recurrent infections,Selective immunoglobulin a deficiency,Sinopulmonary infections

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