Respiratory epithelial adenomatoid hamartoma with inflammatory nasal polyposis

Abstract

Respiratory Epithelial Adenomatoid Hamartoma (REAH) is a type of hamartoma characterized by prominent glandular proliferations lined with ciliated respiratory epithelium originating from the surface epithelium. REAH should be differentiated from inflammatory nasal polyp, inverted papilloma and adenocarcinoma to avoid from more aggressive surgery then is needed for the REAH and to avoid from unnecessary long-term follow-up with medical treatments. In this report, we present a case of REAH who was followed up with topical and systemic steroids for years with the misdiagnosis of inflamatory nasal polyposis and discuss the clinical, radiological and histopathological features of the disease at increasing importance in recent years.  ©

Keywords

• Hamartoma,Nasal polyp,Olfactory cleft,Paranasal computed tomography,Respiratory epithelial adenomatoid

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