Perioperative management of giant symptomatic autosomal dominant polycystic kidney disease: A case report

Year 2017, Volume: 34 Issue: 4, 291 - 295, 10.10.2019

Cengiz Kaya

Abstract

Autosomal dominant polycystic kidney disease
(ADPKD) is an inherited systemic disorder characterized by renal cyst
enlargement which results in abnormal kidney structure and renal insufficiency.
The anaesthesia management of patients with ADPKD is often complex and carries
considerable risks of perioperative complications. Safe and successful anaesthesia
management requires an increased understanding of ADPKD pathophysiology. We report successful
perioperative management of a bilateral open surgical radical nephrectomy on
a male patient with giant symptomatic ADPKD. The patient had chronic renal
failure and extremely large kidneys. We believe that the description and
observations seen in this case will aid in the recognition and anaesthetic
management of this syndrome. 

Keywords

Polycystic kidney disease, Autosomal dominant, Renal failure, Anaesthetic management

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