Melkersson-rosenthal sendromu

Öz

Melkersson-Rosenthal sendromu (MRS) yineleyici periferik fasiyal paralizi, orofasiyal ödem, fissürlü dil triadı ile kendini gösteren nadir bir nöromukokütan granülomatöz hastalıktır. MRS’nin klasik klinik triadının beraber görülmesi nadirdir. Tanısı klinik bulgular ve muayene ile konulur. Yineleyici fasiyal paralizilerin ayırıcı tanısında muhakkak düşünülmesi gerekir. Bu olgu sunumunda MRS’nin klasik triadının bir arada görüldüğü 42 yaşında, kadın hasta sunulmuştur.

Anahtar Kelimeler

• Tekrarlayıcı periferik fasiyal paralizi
• orofasiyal ödem
• fissürlü dil
• nöromukokütan hastalık

Melkersson-rosenthal syndrome

Abstract

The Melkersson-Rosenthal syndrome (MRS) is a rare neuro mucocutaneous granulomatous disease presenting with recurrent peripheral facial paralysis, orofacial oedema, and fissured tongue. The coexistence of the classic clinical triad is rare. Clinical findings and examination make the diagnosis. It should be considered in the differential diagnosis of recurrent facial paralysis. In this case report, a 42-year-old female patient with the classical triad of MRS is presented.

Keywords

• Recurrent peripheral facial palsy
• orofacial oedema
• fissured tongue
• neuro mucocutaneous disease

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