Left ventricular noncompaction: Magnetic resonance imaging findings

Abstract

Left ventricular noncompaction (LVNC) is a rare morphological abnormality of the left ventricular myocardium. It is characterized by trabeculated myocardium with adjacent deep intertrabecular recesses communicating with the left ventricular cavity. Most commonly, the apical and midventricular segments of left ventricle are affected. Patients with LVNC may have no symptoms or present with chest pain, heart failure, and arrhythmias. In the advanced disease stages, heart failure is present in most of the patients. In addition, LVNC can lead to fatal complications, such as embolic events, arrhythmias, and sudden death. These complications can be avoided with early diagnosis and timely treatment of patients at high risk. Herein, we presented an asymptomatic case of LVNC and our aim was to demonstrate the magnetic resonance imaging findings of LVNC.

Keywords

• cardiac MRI,cardiomyopathy,heart failure,myocardial trabeculations,sudden death

Sol ventrikül nonkompaksiyonu: Manyetik rezonans görüntüleme bulguları

Öz

Sol ventrikül nonkompaksiyonu (SVNC), sol ventrikül miyokardının nadir görülen morfolojik bir anomalisidir. Sol ventrikül boşluğu ile komşu derin intertrabeküler oyuklar ile trabeküle halde miyokard ile karakterizedir. Sol ventrikülün apikal ve midventriküler segmentleri en sık etkilenen kesimlerdir. SVNC'li hastalar asemptomatik olabileceği gibi bu hastalarda göğüs ağrısı, kalp yetmezliği ve aritmiler görülebilir. İleri hastalık aşamalarında, çoğu hastada kalp yetmezliği gelişir. Ek olarak, SVNC embolik olaylara, aritmilere ve ani ölüm gibi komplikasyonlara yol açabilir. Bu komplikasyonlar, yüksek riskli hastaların erken tanı ve zamanında tedavisi ile önlenebilir. Biz burada asemptomatik bir SVNC olgusu sunarak SVNC’nin manyetik rezonans görüntüleme bulgularını ortaya koymayı amaçladık.

Anahtar Kelimeler

• kardiyak MR,kardiyomiyopati,kalp yetersizliği,miyokard trabekülasyonları,ani ölüm

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