Left ventricular noncompaction: Magnetic resonance imaging findings

Year 2019, , 343 - 346, 28.05.2019

İbrahim Hasbey Hüseyin Gökhan Yavaş , İsmail Doğu Kılıç Furkan Ufuk

https://doi.org/10.31362/patd.519182

Abstract

Left ventricular noncompaction (LVNC) is a rare morphological
abnormality of the left ventricular myocardium. It is characterized by
trabeculated myocardium with adjacent deep intertrabecular recesses
communicating with the left ventricular cavity. Most commonly, the apical and
midventricular segments of left ventricle are affected. Patients with LVNC may
have no symptoms or present with chest pain, heart failure, and arrhythmias. In
the advanced disease stages, heart failure is present in most of the patients.
In addition, LVNC can lead to fatal complications, such as embolic events,
arrhythmias, and sudden death. These complications can be avoided with early
diagnosis and timely treatment of patients at high risk. Herein, we presented
an asymptomatic case of LVNC and our aim was to demonstrate the magnetic
resonance imaging findings of LVNC.

Keywords

cardiac MRI, cardiomyopathy, heart failure, myocardial trabeculations, sudden death

Sol ventrikül nonkompaksiyonu: Manyetik rezonans görüntüleme bulguları

Abstract

Sol ventrikül nonkompaksiyonu (SVNC), sol ventrikül miyokardının nadir
görülen morfolojik bir anomalisidir. Sol ventrikül boşluğu ile komşu derin
intertrabeküler oyuklar ile trabeküle halde miyokard ile karakterizedir. Sol
ventrikülün apikal ve midventriküler segmentleri en sık etkilenen kesimlerdir.
SVNC'li hastalar asemptomatik olabileceği gibi bu hastalarda göğüs ağrısı, kalp
yetmezliği ve aritmiler görülebilir. İleri hastalık aşamalarında, çoğu hastada
kalp yetmezliği gelişir. Ek olarak, SVNC embolik olaylara, aritmilere ve ani
ölüm gibi komplikasyonlara yol açabilir. Bu komplikasyonlar, yüksek riskli
hastaların erken tanı ve zamanında tedavisi ile önlenebilir. Biz burada
asemptomatik bir SVNC olgusu sunarak SVNC’nin manyetik rezonans görüntüleme
bulgularını ortaya koymayı amaçladık.

Keywords

kardiyak MR, kardiyomiyopati, kalp yetersizliği, miyokard trabekülasyonları, ani ölüm

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