A rare case of thoracoomphalophagus

Year 2019, , 369 - 370, 30.09.2019

Ayhan Atıgan , Ümit Çabuş

https://doi.org/10.31362/patd.570013

Abstract

Conjoined twin is a rarely
seen congenital anomaly together with severe mortality and morbidity. The more
common types of conjoined twins include the thoracoomphalophagus type, where
the fusion is anterior, at the chest and abdomen. We are reporting one case of
conjoined thoracoomphalophagus twins diagnosed by ultrasonography at 10th
gestational week. Multiparous pregnant patient received a conjoined twin
(thoracoomphalophagus) diagnosis after ultrasonographic examination in our
clinic at 10th gestational week and the pregnancy was terminated.  Because of the serious morbidity and
mortality, early diagnosis of conjoined twins by ultrasonographic examination
gives the parents a chance to terminate the pregnancy. 

Keywords

conjoined twin, thoracoomphalophagus, ultrasonography

Nadir görülen bir toraco-omfalopagus olgusu

Abstract

Yapışık ikizler, ciddi
mortalite ve morbidite ile birlikte nadir görülen bir konjenital anomalidir.
Yapışık ikizlerin çeşitleri arasında, göğsün yanı sıra karın füzyonun olduğu
thoracoomphalophagus tipi görülür. Makalemizde 10. haftada ultrasonografi ile
teşhis edilen bir yapışık thoracoomphalophagus ikizleri vakası bildirildi.
Multipar gebe hasta 10. gebelik haftasında kliniğimizde ultrasonografik muayene
sonrası thoracoomphalophagus tanısı aldı ve gebeliği sonlandırıldı.Ciddi
mortalite ve morbiditesi olması sebebiyle, yapışık ikizlere ultrasonografik
muayene ile erken tanı koymak, ebeveynlere hamileliğin sonlandırılması için bir
şans verir. 

Keywords

yapışık ikiz, ultrasonografi, toraco-omfalopagus

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