Lenf Nodu Metastazı Gösteren Adrenal Ganglionörom: Nadir Bir Olgu Sunumu

Year 2024, , 40 - 43, 01.03.2024

Nihal Kiremit , Arzu Tasdemir , Hatice Karaman , Merve Doğan , Turgut Seber

https://doi.org/10.38175/phnx.1300923

Abstract

Ganglionöroma (GN) nöral krestten köken alan nadir görülen benign, iyi diferansiye bir neoplazidir. En sık posterior mediastende görülmekle birlikte adrenal bez de dahil olmak üzere birçok alanda izlenebilir. Posterior mediasten ve retroperiton yerleşimli lezyonlar daha çok çocuk popülasyonda, adrenal ganglionöromalar ise daha çok 4-5. dekadta izlenmektedir. Benign olmalarına rağmen çok nadir lenf nodu ve uzak organ metastazı bildirilmiştir. Bu çalışmada 3 yaşında erkek bir hastada lenf nodu metastazı gösteren, adrenal bez yerleşimli bir ganglionöroma olgusu sunulmuştur.

Keywords

Ganglinörom, Adrenal, Lenf nodu, Metastaz

Adrenal Ganglioneuroma with Lymph Node Metastasis: A Rare Case Report

Abstract

Ganglioneuroma (GN) is a rare benign, well-differentiated neoplasia originating from the neural crest. Although it is most commonly seen in the posterior mediastinum, it can be observed in many areas including the adrenal gland. Lesions located in the posterior mediastinum and retroperitoneum are mostly seen in the pediatric population and adrenal ganglioneuromas are more common in the 4-5. decade. GN is a benign neoplasia but very rarely lymph node and distant organ metastases have been reported. In this study, a case of adrenal gland ganglioneuroma showing lymph node metastasis in a 3-year-old male patient is presented.

Keywords

ganglioneuroma, adrenal, lymph node, metastasis

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