Lymphangioleiomyomatosis-associated spontaneous tension hemopneumothorax in multiple organ involvement tuberculosis

Year 2019, Volume: 10 Issue: 3, 430 - 433, 30.09.2019

Bayram Metin , Mustafa Fatih Erkoç , Sevinç Şahin , Yavuz Selim İntepe

https://doi.org/10.18663/tjcl.477832

Abstract

Tuberosclerosis
complex  is a genetic disorder that can
affect several organs (such as the brain, lungs kidneys, eyes, the heart, bones
and the skin). Pulmonary lymphangioleiomyomatosis is a disease that is mostly
seen among young adult women. It is characterized primarily by the
non-neoplastic atypical proliferation of smooth muscle cells in the lung
parenchyma. Here, we present a case of lymphangioleiomyomatosis-associated
spontaneous hemopneumothorax in a tuberosclerosis patient, which we did not
encounter in the literature.

Keywords

tuberoussclerosis, lymphangioleiomyomatosis, hemopneumothorax

Multi organ tutulumlu tüberosklerozda lenfanjiyoleiyomiyomatozise bağlı spontan tansiyon hemopnömotoraks olgusu

Abstract

Tuberosklerozis kompleksi, beyin, akciğer, böbrek,
göz, kalp, kemik ve deri gibi organları etkileyebilen genetik bir hastalıktır. Pulmoner
lenfanjiyoleiyomiyomatozis daha çok genç erişkin bayanlarda görülen bir
hastalıktır. Akciğer parankimindeki düz kas hücrelerinin neoplastik olmayan
atipik proliferasyonu ile karakterizedir. Biz burada literatürde
karşılaşmadığımız tuberosklerozis hastasında lenfanjiyoleiyomiyomatozise bağlı
spontan hemopnömotoraks olgusunu sunuyoruz.

Keywords

tuberosklerozis, lenfanjiyoleiyomiyomatozis, hemopnömotoraks

References

• 1. Tsai C-F, Hsiao C-H, Lee J-M, et al. Video-assisted thoracoscopic surgery for recurrent pneumothorax in pulmonary lymphangioleimyomatosis with tuberous sclerosis complex. Journal of Cardiothoracic Surgery 2013, 8:101
• 2. Northrup H, Krueger DA. Updated diagnostic criteria for tuberous sclerosis complex 2012. Pediatr Neurol 2013; 49: 243–54.
• 3. Kwiatkowski DJ, Whittemore VH, Thiele EA. Tuberous Sclerosis Complex, Genes, Clinical Features and Therapeutics. Wiley-VCH2010; 1: 432.
• 4. Nishida C, Yatera K, Kido T, et al. Two Cases of Tuberous Sclerosis Complex Suggestive of Complicating Multifocal Micronodular Pneumocyte Hyperplasia: A Case Report. J UOEH 2017; 39: 133-141.
• 5. Zhou B, Guo Q, Zhou H et al. Pulmonary lymphangioleiomyomatosis in a 46-year-old female: A case report and review of the literatüre. Biomedical Reports 2016; 4: 719-22.
• 6. Lama A, Ferreiro L, Golpe A et al. Characteristics of Patients with Lymphangioleiomyomatosis and Pleural Effusion: A Systematic Review. Respiration 2016; 91: 256-64
• 7. Apilioğulları B, Esme H. Treatment of the spontaneous hemopneumothorax; 2 cases. J Surg Arts 2009; 2: 24-28.
• 8. Ranke FMV, Faria IM, Zanetti G, et al. Imaging of tuberous sclerosis complex: a pictorial review. Radiol Bras 2017; 50: 48–54
• 9. Oesterling JE, Fishman EK, Goldman SM, Marshall FF. The management of renal angiomyolipoma. J Urol 1986; 135: 1121–24.
• 10. Gosein MA, Ameeral A, Konduru SKP et al.Tuberous sclerosis presenting with spontaneous pneumothorax secondary to lymphangioleiomyomatosis; previously mistaken for asthma. BMJ Case Rep 2013.