Atriyal flattere neden olan hamak mitral kapak: Üç aylık bebek olgu

Öz

Hamak mitral kapak oldukça nadir görülen doğuştan mitral kapak hastalığıdır Çocuklarda mitral darlık ya da yetersizliğe neden olabilir Hastalar sıklıkla kliniğe kalp yetersizliği bulguları ile gelirler ancak ani ölüm de görülebilmektedir Kliniğimize kalp yetersizliği bulguları ile başvuran üç aylık kız bebeğe yapılan incelemeler sonucunda; hamak mitral kapak sol atriyal genişleme önemli mitral kapak yetersizliği ve atriyal flatter tanıları koyuldu Erişkinlerin aksine bu yaş grubunda atriyal flatter çok nadir görülen bir aritmidir Bu olguyu hamak mitral kapağa bağlı gelişen atriyal flatter olgusunun daha önce sunulmamış olması nedeni ile sunduk.

Anahtar Kelimeler

• Atriyal flatter
• hamak mitral kapak
• mitral yetersizlik

Hammock mitral valve as a cause of atrial flutter: A 3 month old infant case

Abstract

Hammock mitral valve is a very rare congenital valve disorder It may lead to mitral stenosis or insufficiency in the pediatric age group These patients generally present with the symptoms of congestive heart failure or sometimes sudden death may occur Our case was a 3 month old female infant who presented to our clinic with the symptoms of heart failure Her cardiac evaluation revealed hammock mitral valve left atrial dilatation severe mitral valve insufficiency and atrial flutter In contrast to adult patients atrial flutter is a very rare type of cardiac aryhtmia in the pediatric age group We present this case because no such case with atrial flutter resulting from hammock mitral valve has been reported in the literature Turk Arch Ped 2013; 48: 244 247

Keywords

• Atrial flutter, hammock mitral valve, mitral insufficiency

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