Pulmonary arteriovenous malformation associated with Osler Weber Rendu syndrome

Abstract

Osler Weber Rendu syndrome is a relatively common vascular displasia characterized by telangiectases of the skin mucosa and visceral organs and arteriovenous malformations in children We reported a 9 year old boy diagnosed as Osler Weber Rendu syndrome with his

Keywords

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Osler-Weber-Rendu sendromu ile ilişkili pulmoner arteriyovenöz malformasyon

Öz

Osler Weber Rendu sendromu çocuklarda göreceli sık görülen; cilt mukoza ve iç organlarda telanjiektazi ve arteriyovenöz malformasyonlarla seyreden vasküler bir displazidir Bu yazıda akut romatizmal kardit atağı sırasında santral siyanoz çomak parmak yüzde burun mukozasında telanjiektaziler ve sağ akciğerde arteriyovenöz malformasyonu saptanan ve Osler Weber Rendu sendromu tanısı alan dokuz yaşında bir erkek olgu sunuldu Akut romatizmal kardit atağı geçtikten sonra olguya kalp kateterizasyonu yapılarak arteriyovenöz malformasyona ldquo;coil rdquo; embolizasyonu uygulandı.

Anahtar Kelimeler

• Osler-Weber-Rendu sendromu
• pulmoner arteriyovenöz malformasyon
• romatizmal kalp hastalığı
• siyanoz

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