Malignant peripheral nerve sheath tumor of the parotid gland

Year 2007, Volume: 17 Issue: 1, 53 - 57, 12.01.2007

İsmet Aslan Çağatay Oysu Menekşe Bilge Bilgiç Bora Başaran Engin Yazıcıoğlu

Abstract

Malignant peripheral nerve sheath tumors originating from the parotid gland are extremely rare. A 76-year- old male patient undervvent an incisional biopsy tor an ulcerated mass in the anteroinferior aspect of the left auricle. The diagnosis was made as malignant mes- enchymal tissue sarcoma, but the patient refused treatment. Upon Progressive growth of the mass with- in two months, he undervvent a partial parotid gland resection. After three months, he was referred to our clinic with an aggressively grovving parotid mass. Total parotidectomy and radical neck dissection were per- formed. Histopathological diagnosis was malignant peripheral nerve sheath tumor. Follovving radiotherapy, has been under follow-up for five years.

Keywords

Head and neck neoplasms, nerve sheath tumors/pathology/surgery, parotid neoplasms

Parotis bezinin habis periferik sinir k›l›f› tümörü

Abstract

Parotis bezinden habis periferik sinir kılıfı tümörü gelişimi son derece nadirdir. Yetmiş altı yaşında erkek hastaya, sol kulak ön-alt bölümünde ülsera- tif kitle nedeniyle daha önce yapılan biyopsi sonu- cunda malign mezenkimal tümör tanısı konmuş, ancak hasta tedaviyi reddetmişti. Sonraki iki ay içinde kitlenin büyümesi nedeniyle parsiyel parotis rezeksiyonu yapılmıştı. Hasta üç ay sonra parotis- te aşırı büyüme nedeniyle kliniğimize başvurdu. Hastaya tedavi olarak total parotidektomi ve radi- kal boyun diseksiyonu uygulandı. Histopatolojik ta- nı malign periferik sinir kılıfı tümörü olarak kondu. Radyoterapi uygulanan hasta beş yıldır takip edilmektedir

Keywords

Baş-boyun neoplazileri, sinir kılıfı tümörü/patoloji/cerrahi, parotis neoplazileri

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