A rare cause of exophthalmos: cemento-ossifying fibroma

Year 2008, Volume: 18 Issue: 3, 185 - 187, 25.06.2008

Melda Apaydın Çağlar Çallı Bengü Günay Yardım Ayşegül Sarsılmaz Makbule Varer Engin Uluç

Abstract

Cemento-ossifying fibroma is a benign fibroosseous lesion that contains fibrous tissue and calcified tissue resembling bone, cementum or both. It is frequently seen in the mandibula and maxilla, but it may rarely affect the ethmoid sinus. In this report, we presented computed tomography findings of an ossifying fibroma of the ethmoid sinus associated with exophthalmos. A 25-year-old woman presented with complaints of exophthalmos, headache, and nasal congestion of six-month history. Physical examination showed a firm mass on the right side of the nasal septum and right-sided exophthalmos. Eye movements, vision, and the fundus were normal. Axial and coronal computed tomography scans showed a well-delineated, round mass, 4x4.5x3 cm in size, in the right ethmoid sinus, extending from the right orbital rim to the right nasal cavity. Near-total excision of the mass was performed by a lateral rhinotomy and medial maxillotomy approach. Based on histologic and radiological findings, the diagnosis was made as ossifying fibroma.

Keywords

Bone neoplasms, ethmoid sinus, exophthalmos/etiology, fibroma, ossifying/diagnosis/pathology, paranasal sinus neoplasms

Ekzoftalmusun nadir bir nedeni: Semento-ossifiye fibroma

Abstract

Semento-ossifiye fibroma içinde fibröz doku ve kemik, sementum ya da her ikisini andıran kalsifi- ye doku içeren benign fibro-osseöz bir lezyondur. Sıklıkla mandibula ve maksillayı, nadiren de etmoid sinüsü etkiler. Bu yazıda, etmoid sinüste gelişen ve ekzoftalmus oluşturan ossifiye fibromaya ait bilgisa- yarlı tomografi bulguları sunuldu. Yirmi beş yaşın- daki bir kadın hasta, altı aydır var olan ekzoftalmus, baş ağrısı ve burunda konjesyon yakınmalarıyla başvurdu. Fizik muayenede, nazal septumun sağ tarafında sert bir kitle ve aynı tarafta ekzoftalmus saptandı. Göz hareketleri, görme ve fundus normal bulundu. Aksiyel ve koronal bilgisayarlı tomografi görüntülerinde, sağ etmoid sinüste, sınırları belirgin, yuvarlak ve sağ göz çukuru kenarından sağ nazal kaviteye kadar uzanan, 4x4.5x3 cm büyüklüğünde bir kitle görüldü. Kitle lateral rinotomi ve medial mak- sillotomi yaklaşımıyla tama yakın çıkarıldı. Histolojik ve radyolojik bulgular ışığında tanı ossifiye fibroma olarak kondu

Keywords

Kemik neoplazileri, etmoid sinüs, ekzoftalmus/etyoloji, fibroma, ossifiye/tanı/patoloji, paranazal sinüs neoplazileri

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