Bartholin bezi lokalizasyonunda nadir görülen bir kitle: Leiomyosarkom

Abstract

Vulvar leiomyosarkom, vulvanın düz kas dokusundan kaynaklanan nadir bir malign tümördür; ancak vulvar sarkomlar arasında en sık görülen tiptir. Genellikle iyi huylu bir lezyon izlenimi verdiğinden, yanlış tanıya ve tedavide gecikmelere yol açabilir. Bu yazıda, başlangıçta anal apse veya Bartholin apsesi olarak değerlendirilen bir olgu sunulmaktadır. Görüntüleme yöntemleriyle yapılan incelemede, kistik yapıdan ziyade miyomu andıran solid özellikte bir vulvar kitle saptanmıştır. Kitlenin geniş lokal eksizyonunun ardından gerçekleştirilen immünohistokimyasal boyama ve patolojik inceleme sonucunda vulvar leiomyosarkom tanısı konmuştur. Güncel literatürde, vulvar leiomyosarkomların oldukça nadir görülmesi nedeniyle standart bir tedavi algoritması bulunmadığı vurgulanmaktadır. Bu olguda, disiplinler arası iş birliğiyle hasta bazlı kişiselleştirilmiş bir tedavi yaklaşımı benimsenmiş ve vaka, mevcut literatürdeki yönetim stratejileriyle birlikte değerlendirilmiştir.

Keywords

• leiomyosarcoma
• vulvar sarcoma
• vulvar leiomyosarcoma
• Bartholin cyst

A rare mass on the localization of Bartholin gland: Leiomyosarcoma

Abstract

Vulvar leiomyosarcoma is a rare malignant tumor of the vulva originating from smooth muscle, yet it is the most common type of vulvar sarcoma. It often presents as a benign lesion, which can lead to misdiagnosis and delays in appropriate treatment. We present a case that was initially suspected to be an anal abscess or Bartholin gland abscess. Imaging revealed a solid vulvar mass with fibroid-like characteristics rather than a cystic structure. Following wide local excision, histopathological examination and immunohistochemical staining confirmed the diagnosis of vulvar leiomyosarcoma. Current literature emphasizes the lack of a standardized treatment algorithm due to the rarity of this tumor. This case highlights a personalized treatment approach enabled by interdisciplinary collaboration.

Keywords

• leiomyosarcoma
• vulvar sarcoma
• vulvar leiomyosarcoma
• Bartholin cyst

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