VULVAR RABDOMYOSARKOM: BİR OLGU SUNUMU

Abstract

Vulvar tümörler nadir görülür, vulvar sarkomlar ise tüm vulvar tümörlerin %1-2’sini oluflturur. Biz klini¤imizde palyatif radyoterapi alan ve agresif seyreden bir vulvar alveoler tip rabdomyosarkom vakas›n› sunmay› amaçlad›k. Yirmi yafl›nda hasta genital bölgede flifllik flikayetiyle baflvurmufltu. Radikal hemivulvektomi ve sa¤ inguinal lenfadenoktomi yap›lan hastan›n postoperatif patoloji raporu alveoler rabdomyosarkom olarak raporlanm›flt›. Postoperatif kemoterapi ve radyoterapi alan hastan›n tedavinin tamamlanmas›ndan bir ay sonra exitus oldu. Nadir görülen ve agresif seyreden vulvar alveoler rabdomyosarkom vakas› sunulmufl ve literatür bilgileri eflli¤inde tedavisi ve prognozu tart›fl›lm›flt›r.

Abstract

Vulvar tumors are uncommon, among them vulvar sarcomas represent only 1-2% of all vulvar malignancies. We aimed to present an agressive vulvar alveolar type rhabdomyosarcoma that was treated with palliative radiotherapy at our clinic. A 20-years-old patient presented with a mass on genitalia. Radical hemivulvectomy and inguinal lymphadenectomy was performed and postoperative histopathology was reported as alveolar rhabdomyosarcoma. Postoperative chemotherapy and radiotherapy was administered, one month after completion of treatment she died. A case of vulvar alveolar rhabdomyosarcoma which is uncommon and agressive is presented and the treatment and prognosis is discussed with the literature review.