GÖĞÜS ÖN DUVARI TUTULUMU VE SKALP METASTAZI İLE SEYREDEN NADİR BİR HEMANJİYOPERİSTOM OLGUSU

Year 2011, Volume: 19 Issue: 2, 88 - 90, 01.08.2011

Burak Ersoy Serdar Evman Mehmet Bayramiçli Mustafa Yüksel

Abstract

Kapiler ve venüllerin etrafındaki Zimmermann perisitlerinden köken alan vasküler bir tümör olarak tarif edilen hemanjiyoperistom daha çok 50-70 yaşları arasında karşılaşılan nadir bir mezenkimal tümördür. Erişkinlerde en sık alt ekstremite ve retroperitonda, pediyatrik yaş grubu hastalarında ise alt ekstremite ve baş-boyun bölgesinde görülen hemanjiyoperistom yavaş büyüme göstermekte ve yüksel lokal nüks riski taşımaktadır. Bu çalışmada, 18 yaşında göğüs ön duvarı tutulumu ile ilk kez farkedilen, takipleri sırasında lokal nüks, vertebra ve skalp metastazı için ek operasyonlara gereksinim oluşturan nadir bir hemanjiyoperistom olgusu sunulmuştur.

Keywords

hemanjiyoperistom, skalp, göğüs ön duvarı, metastaz

A RARE CASE OF HEMANGIOPERICYTOMA WITH ANTERIOR CHEST WALL INVOLVEMENT AND SCALP METASTASIS

Abstract

Hemangiopericytoma is described as a distinct entity of vascular tumor which originates from the contractile pericytes of Zimmermann around capillaries and venules. These rare mesenchymal tumors may develop at almost any age, but usually they occur during the fifth or seventh decade. In adults, the common sites of origin are in the lower extremity and retroperitoneum, whereas in children the tumors have a predilection for the head and neck region and lower extremities. It usually demonstrates a slow progression in size with high local recurrence rate following surgical intervention. A rare case of hemangiopericytoma in a 18-year-old male patient is presented, who was first diagnosed with hemangiopericytoma involving anterior chest wall and underwent later on further surgical operations owing to the emergence of local recurrence and metastasis to his vertebra and scalp.

Keywords

hemangiopericytoma, scalp, anterior chestwall, metastasis

References

• 1. Stout AP, Murray MR. Hemangiopericytoma: a vascular tumor featuring Zimmerman’s pericytes. Ann Surg 1942 Jul;116(1):26- 33.
• 2. Plukker JT, Koops HS, Molenaar I, Vermey A, ten Kate LP, Oldhoff J.. Malignant hemangiopericytoma in three kindred members of one family. Cancer 1988 Feb 15;61(4):841–844.
• 3. Guthrie BL, Ebersold MJ, Scheithauer BW, Shaw EG. Meningeal hemangiopericytoma: histopathological features, treatment, and long-term follow-up of 44 cases. Neurosurgery 1989;25: 514–522.
• 4. Chnaris A, Barbetakis N, Efstathiou A, Fessatidis I. Primary mediastinal hemangiopericytoma. World J Surg Oncol. 2006 Apr 27;4:23.
• 5. Suzuki H, Haga Y, Oguro K, Shinoda S, Masuzawa T, Kanai N. Intracranial hemangiopericytoma with extracranial metastasis occurring after 22 years. Neurol Med Chir 2002 Jul;42(7):297–300.