Ender bir olgu: Yeniden açılan foramen ovale nedeniyle sağdan sola şanta yol açan orta düzeyde gradyanlı pulmoner supravalvuler stenoz

Öz

Sağdan sola şantın eşlik ettiği supravalvuler pulmoner stenoz erişkinlerde ender görülen bir ekokardiyografi bulgusudur. Önceden tanısı konmamış patent foramen ovaleden gelişen sağdan sola şantın eşlik ettiği supravalvuler pulmoner stenoz gelişen hastanın olgusu sunulmuştur. Bu konjenital anomali, valvuler pulmoner stenozdan tedavi yöntemlerinin ayrı olmasından dolayı ayırıcı tanısı yapılmalıdır.

Anahtar Kelimeler

• Pulmoner, supervalvular stenoz, foramen ovale

A rare case: Pulmonary supravalvular stenosis with moderate gradient causing an atrial right to left shunt across the reopened foramen ovale

Abstract

Supravalvular pulmonary stenosis accompanied by a right to left shunt is a rare echocardiographic finding in adults. We report a case of adult pulmonary supravalvular membranous stenosis with an atrial right to left shunt developed through a previously undiagnosed patent foramen ovale (PFO).The peculiarity of our case is that foramen ovale reopened despite a moderate pulmonary trunk gradient over a six year period. This congenital anomaly is a condition to be differentiated from valvular pulmonary stenosis as both anomalies require different modalities of treatment (surgical or catheter).

Keywords

• Pulmonary,supervalvular stenosis, foramen ovale

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