Hidronefrotik fonksiyon göstermeyen böbrekli genç erkek olguda mikst epitelyal stromal tümör: Literatür bulguları ile karşılaştırma

Abstract

Mikst epiteliyal stromal tümör (MEST) ailesi, kistik komponenti baskın olan erişkin kistik nefroma ve solid komponent baskın MEST’ten oluşmaktadır. MEST, epitelyal ve stromal komponente sahip böbreğin nadir görülen benign, bifazik tümörüdür. Karın ağrısı ile başvuran 24 yaşında erkek olgunun tetkiklerinde grade 4 hidronefroz saptandı. Nefrektomi piyesinin mikroskobik incelemesinde, ovaryan stroma içerisinde değişken çaplarda küboidal epitel ile döşeli tubul yapıları mevcuttu. Olguya, morfolojik ve immunohistokimyasal bulgular ile MEST tanısı verildi. Genç erkeklerde sınırlı sayıda saptanan ve daha önce fonksiyon göstermeyen böbrek ile birlikteliği bildirilmeyen MEST tanısı verdiğimiz olgumuzun klinik ve histopatolojik özelliklerini literatür verileri ile karşılaştırmayı amaçladık.

Keywords

• Mikst epitelyal stromal tümör
• nonfonksiyone
• böbrek
• erkek

Mixed epithelial and stromal tumor in a young male case with hydronephrotic nonfunctional kidney: Comparison with literature findings

Abstract

The mixed epithelial and stromal tumor (MEST) family is comprised of adult cystic nephroma with a dominant cystic component and MEST with a dominant solid component. MEST is the rarely observed benign, biphasic tumor of the kidney with a mixed epithelial and stromal component. In the examinations of a 24-year-old male patient who presented with abdominal pain, grade-4 hydronephrosis was detected. In the microscopic examination of his nephrectomy specimen, there were tubular structures with cuboidal epithelium in different diameters within the ovarian stroma. The patient was diagnosed with MEST via morphological and immunohistochemical findings. We aimed at comparing the clinical and histopathological characteristics of our case, which we diagnosed with MEST, which is encountered in limited numbers in young men and has never been reported together with a nonfunctional kidney before, to the literature data.

Keywords

• Mixed Epithelial and Stromal tumor
• nonfunctional
• kidney
• male

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