Nadir görülen dev retroperitoneal liposarkom: Olgu sunumu

Year 2015, Volume: 10 Issue: 3, 47 - 49, 01.08.2015

Fatih Akdemir¹ Aylin Kılıç Yazgan² Muhammet Fuat Özcan¹ Emrah Okulu¹ Asım Özayar¹ Serdar Çakmak¹ Mustafa Aldemir¹ Kemal Ener

Abstract

Yumuşak doku sarkomları, erişkinlerde görülen tümörlerin %1’ini oluşturmakta ve bunların yaklaşık %10-20’si retroperitoneal bölgede görülmektedir. Retroperitoneal liposarkomlar, oldukça ender görülen malign tümörler olup, prognozu oldukça kötüdür. Büyük boyutlara ulaşmadan genellikle semptom vermezler. Retroperitoneal liposarkomların geniş cerrahi rezeksiyonu sırasında, bazı organların kitleyle beraber çıkarılması gerekebilmektedir. Bu olgu sunumunda, nadir görülen ve agresif bir klinik seyir gösteren andiferansiye liposarkomu, literatür bilgileri eşliğinde sunmayı amaçlamaktayız

Keywords

Retroperiton , andiferansiye liposarkom , radikal rezeksiyon

A rare case report: Giant retroperitoneal liposarcoma

Abstract

Soft tissue sarcomas comprise 1% of adulthood tumors, and about 10-20% of them are located in the retroperitoneum. Retroperitoneal liposarcomas are rarely seen malignancies with poor prognosis. They remain asymptomatic unless they grow up to extremely large sizes. The extensive surgical resection of these tumors may necessitate the resection of various organs involved with the tumor. Herein, we report a rarely seen entity, with agressive clinical progress by reviewing the literature

Keywords

retroperitoneum , undifferantiated liposarcoma , radical resection

References

• Porter GA, Baxter NN, Pisers PW. Retroperitoneal sarco- ma: a population-based analysis of epidemiology, surgery and radiotherapy. J Clin Oncol, suppl. 2005;23:9025.
• Mack TM. Sarcomas and other malignancies of soft tissue, retroperitoneum, peritoneum, pleura, heart, mediastinum and spleen. Cancer 1995;75:211-44.
• Levis JJ, Leung D, Woodruff JM: Retroperitoneal Soft Tis- sue Sarcoma. Annals of Surgery 1998;228:335-65.
• Inoue K, Higaki Y, Yoshida H. Giant retroperitoneal lipo- sarcoma. Int J Urol 2005;12:220-2.
• Sundaram M, McLeod RA. MR imaging of tumor and tu- morlike lesions of bone and soft tissue. AJR Am J Roentge- nol 1990;155:817-24.
• Kursh DE: Retroperitoneal Tumours. Resnick MI, No- vick AC (eds); Urology Secrets, Hanley and Belfus INC 1995;70-1.
• Shahaji C, Amit P, Prashant P, Sachin T. Giant retroperi- toneal liposarcoma: a case report Case Rep Oncol Med 2012;2012:869409.
• Ferrario T, Karakousis CP. Retroperitoneal sarcomas: gra- de and survival. Arch Surg 2003;138:248-51.
• Strauss DC, Hayes AJ, Thomas JM. Retroperitoneal tu- mors: review of management. Ann R Coll Surg Engl 2011; 93:275-80.
• Singer S, Antonescu CR, Riedel E, Brennan MF. Histologic subtype and margin of resection predict pattern of recur- rence and survival for retroperitoneal liposarcoma. Ann Surg 2003;238:358-70.
• Gönen M, Sevin G: Elli Yaşındaki Bir Hastada Görülen Dev Retroperitoneal Liposarkom Olgusu. Üroloji Bülteni 2002;13:111-2.
• Weiss SW, Rao VK. Well-differentiated liposarcoma (atypi- cal lipoma) of deep soft tissue of the extremities, retroperi- toneum, and miscellaneous sites. A follow-up study of 92 cases with analysis of the incidence of “dedifferentiation”. Am J Surg Pathol 1992;16 :1051-8.
• Goss G, Demetri G. Medical management of unresectable, recurrent low-grade retroperitoneal liposarcoma: integra- tion of cytotoxic and non-cytotoxic therapies into multi- modality care 2000;9:53-9.