Kawasaki Hastalığında Güncel Gelişmeler

Abstract

Kawasaki hastalığı, daha önceleri mukokütanöz lenf nodu hastalığı veya infantil poliarteritis nodoza olarak da bilinen çocuklarda görülen akut febril bir hastalıktır. Hastalık, nedeni tam olarak bilinmeyen sistemik bir vaskülit olarak orta çaplı damar tutulumu ile seyreder ve çoğunlukla 5 yaş altı çocuklarda görülür. Kan damarları, cilt, muköz membranlar ve lenf nodları başta olmak üzere birçok organ sistemi etkilenir. En Nadir fakat en önemli etkilerinden biri kalp üzerinedir, tedavi edilmeyen çocuklarda fatal koroner arter anevrizmalarına neden olabilmektedir. Bu nedenle tanının erken konması, tedavinin zamanında ve uygun bir şekilde planlanması oldukça önemlidir. Bu derlemede ülkemizde de önemli bir morbidite nedeni olan Kawasaki hastalığının tanı, tedavi süreçleri ve prognostik özellikleri tartışılmıştır.

Keywords

• Kawasaki,mukokutanöz lenf nodu hastalığı,tedavi

Recent Advances in Kawasaki Disease

Abstract

Kawasaki disease is an acute febrile disease inchildren formerly known as mucocutaneous lymphnode disease or infantilepolyarteritis nodosa. The disease, a systemic vasculitis of unknown etiology, in which the medium-sized blood vessels are affected, is frequently seen in children under five years of age. Organ systems, mainly the blood vessels, skin, mucous membranes, and lymph nodes are involved. The rarest but the most serious effect of the disease is on the heart, where it can cause fatal coronary artery aneurysms in untreated children. Therefore, early diagnosis, timely and appropriate treatment approach is very important. In this review, diagnosis, treatment processes and prognostic features of Kawasaki disease, also an important cause of morbidity in our country, were discussed.

Keywords

• Kawasaki,Mucocutenous lymph node syndrome,treatment

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