Öz
PFAPA syndrome periodic fever, aphthous stomatitis, pharyngitis, cervical adenitis is a pediatric periodic disease characterised by recurrent febrile episodes. This syndrome usually observed under 5 years of age and common in boys. In this case report, a 4 year old boy with complained of recurrent attacks of fever, tonsillitis and cervical lenfadenitis is presented. The attacks had recurred every 20-25 days. The attacks of the patient dramatically resolved after a single dose of metilprednisolon.
Anahtar Kelimeler
Kaynakça
- Feder HM Jr. Periodic fever, aphthous stomatitis, pharyngitis, adenitis:a clinical review of a new synd- rome. Curr Opin Pediatr 2000;12:253-56
- John CC, Gilsdorf JR. Recurrent fever in children. Ped İnfect Dis J 2002;21:1071-77
- Scholl PR. Periodic fever syndrome. Curr Opin Pedi- atr 2000;563-66
- Thomas KT, Feder HM, Lawton AR, Edwards KM. Peridic fever ssyndrome in children. J Pediatr ;135:15-21
- Silvia Stojanov, Florian Hoffmann, Anja Kéry, Ellen D Renner, Dominik Hartl, Peter Lohse, Kristina Huss, Peter Fraunberger, James D Malley, Stephanie Zelle- rer, Michael H Albert, Bernd H Belohradsky. Cytokine profile in PFAPA syndrome suggests continuous inf- lammation and reduced anti- inflammatory response. Eur Cytokine Netw 2006;17:90-97
- Tasher D, Somekh E, Dalal I. PFAPA syndrome:new clinical aspects disclosed. Arch Dis Child 2006;9:981
- Forsvoll JA, Oymar K. C reaktive protein in the periodic fever, aphthous stomatitis, pharyngitis and cervical adenitis (PFAPA) syndrome. Acta Pediatr ;96:1670-73
- Berlucchı M, Meini A, Plebani A, Bonvini MG, Lom- bardi D, Nicolai P. Update on treatment of Marshall’s Syndrome (PFAPA syndrome):Report of five cases with review of the literature. Ann Otol Rhinol Laryngol ; 112: 365-69
- Tasher D, Stein M, Dalal I; Somekh E. Colchicine propylaxis for frequent periodic fever, aphthous sto- matitis, pharyngitis and adenitis episodes. Acta paedi- atr 2008;97:1090-92.
Öz
PFAPA sendromu periyodic ateş, aftöz stomatit, farenjit ve servikal lenfadenit tekrarlayan ateş atakları ile karekterize bir periyodik çocukluk çağı hastalığıdır. Bu sendrom genellikle 5 yaş altı ve erkek çocuklarda daha fazla gözükmektedir. Bu yazıda 4 yaşında 20-25 günde bir tekrarlayan ateş, tonsillit ve servikal lenfadenit ile başvuran bir erkek çocuk sunuldu. Ataklar tek doz metilprednizolon tedavisi ile dramatik olarak düzeldi.
Anahtar Kelimeler
Kaynakça
- Feder HM Jr. Periodic fever, aphthous stomatitis, pharyngitis, adenitis:a clinical review of a new synd- rome. Curr Opin Pediatr 2000;12:253-56
- John CC, Gilsdorf JR. Recurrent fever in children. Ped İnfect Dis J 2002;21:1071-77
- Scholl PR. Periodic fever syndrome. Curr Opin Pedi- atr 2000;563-66
- Thomas KT, Feder HM, Lawton AR, Edwards KM. Peridic fever ssyndrome in children. J Pediatr ;135:15-21
- Silvia Stojanov, Florian Hoffmann, Anja Kéry, Ellen D Renner, Dominik Hartl, Peter Lohse, Kristina Huss, Peter Fraunberger, James D Malley, Stephanie Zelle- rer, Michael H Albert, Bernd H Belohradsky. Cytokine profile in PFAPA syndrome suggests continuous inf- lammation and reduced anti- inflammatory response. Eur Cytokine Netw 2006;17:90-97
- Tasher D, Somekh E, Dalal I. PFAPA syndrome:new clinical aspects disclosed. Arch Dis Child 2006;9:981
- Forsvoll JA, Oymar K. C reaktive protein in the periodic fever, aphthous stomatitis, pharyngitis and cervical adenitis (PFAPA) syndrome. Acta Pediatr ;96:1670-73
- Berlucchı M, Meini A, Plebani A, Bonvini MG, Lom- bardi D, Nicolai P. Update on treatment of Marshall’s Syndrome (PFAPA syndrome):Report of five cases with review of the literature. Ann Otol Rhinol Laryngol ; 112: 365-69
- Tasher D, Stein M, Dalal I; Somekh E. Colchicine propylaxis for frequent periodic fever, aphthous sto- matitis, pharyngitis and adenitis episodes. Acta paedi- atr 2008;97:1090-92.
Ayrıntılar
| Birincil Dil | Türkçe |
|---|---|
| Bölüm | Olgu Sunumu |
| Yazarlar | |
| Yayımlanma Tarihi | 1 Mayıs 2013 |
| Yayımlandığı Sayı | Yıl 2013 Cilt: 2 Sayı: 2 |