Renal Amyloıd- Ourstııcasrı A And Deafness
Abstract
A 48 - year -old patient with progressive bilateral perceptive deafness, bouts ol fever, chronic urticaria, pes cavus and rena! amyloidosis is derseribed. The case was characterized by long duration (14 years) with initial involment of the kidneys and subseguent development of deafness. This represents the third (sporadic) instance of the clinical syndrome initialliy described by Muckle and Wells.
Keywords
Chronic urticaria, Renal amyloidosis, Progressive hearing loss, Muckle-Wells syndrome, Autoinflammatory syndrome
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