Chiari Malformasyonu Olmayan Spinal Disrafiye Bağlı Holokord Siringomiyeli: Vaka Sunumu

Year 2026, Volume: 15 Issue: 1 , 195 - 199 , 28.02.2026

Ali Samet Topsakal , Mehmet Orbay Bıyık , Mehmet Aktoklu , Ertuğrul Çakır

https://doi.org/10.53424/balikesirsbd.1783164

https://izlik.org/JA63DH96XT

Abstract

Siringomiyeli, miyelopatiye neden olan omuriliğin kistik genişlemesidir. Yaygın olarak kullanılan sınıflandırma, patofizyolojik mekanizmalar dışında anatomik özelliklere veya patojene dayanan bir sınıflandırmadır. Birçok patofizyolojik teori arasında en yaygın kabul göreni, alt araknoid boşluklardaki beyin omurilik sıvısı (BOS) akışındaki bozuklukların akış hızını bozarak syrinkse yol açmasıdır. İdiyopatik olarak ortaya çıkabilmesine rağmen, Tip 1 ve 2 Chiari, Dandy-Walker sendromu serebellar ektopi baziler izlenim baziler araknoidit, posterior fossa tümörleri ve araknoid kistler, medulla spinalis tümörleri, spinal travma ve enfeksiyonlar en sık nedenler arasındadır. Siringomiyeli hastalarda en sık tip 1 Chiari malformasyonu ile birlikte görülür. Bu bilgiler ışığında, tip 1 Chiari malformasyonu olmaksızın nadir görülen gergin kord ve holokord siringomiyeli olgusunu sunuyoruz. Hastanın tedavi süreci hakkında bilgi vererek literatüre katkı sağlamayı amaçladık.

Keywords

Malfırmasyon Arnold-Chiari , Gergin Kord Sendromu , Şiringomyeli

Ethical Statement

Çalışma retrospektif olarak yürütülmüştür ve anonimleştirilmiş veriler kullanıldığı için etik kurul onayı gerektirmez. Bu makale Helsinki Bildirgesi ilkelerine uygun olarak hazırlanmıştır ve etik kurul onayı gerektirmez.

Supporting Institution

Yok.

Thanks

Yazarlar, bu çalışmaya katkıda bulunan herkese içten teşekkürlerini sunar.

Holocord Syringomyelia due to Spinal Dysraphism without Chiari Malformation - A Case Report

https://izlik.org/JA63DH96XT

Abstract

Syringomyelia is a cystic enlargement of the spinal cord that causes myelopathy. The commonly used classification is one based on anatomical features or pathogen other than pathophysiological mechanisms. Among the many pathophysiological theories, the most widely accepted is that disturbances in cerebrospinal fluid (CSF) flow in the lower arachnoid spaces disrupt flow velocity leading to syrinx. Although it may appear idiopathically, Type 1 and 2 Chiari, the Dandy-Walker syndrome cerebellar ectopia basilar impression basilar arachnoiditis, posterior fossa tumors and arachnoid cysts, medulla spinalis tumors, spinal trauma and infections are among the most common causes. Syringomyelia is mostly seen with type 1 Chiari malformation in patients. Based on this information, we present this rare patient with tethered cord and holocord syringomyelia without type 1 Chiari malformation. We aimed to contribute to the literature by providing information about the treatment process of the patient.

Keywords

Malformation Arnold-Chiari , Tethered Cord Syndrome , Syringomyelia

Ethical Statement

The study was conducted retrospectively and does not require ethics committee approval as it uses anonymised data. This article has been prepared in accordance with the principles of the Declaration of Helsinki and does not require ethics committee approval.

Supporting Institution

No funding.

Thanks

The authors would like to extend their sincere thanks to anyone who contributed to this study.

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