Evaluation of congenital anomalies accompanying to gastrointestinal system surgical pathologies

Murat Konak; Ahmet Sert; Metin Gündüz; Hanifi Soylu; Saime Sündüs Uygun

doi:10.17826/cumj.458835

TR EN

Gastrointestinal sistem cerrahi patolojilerine eşlik eden konjenital anomalilerin değerlendirilmesi

Öz

Amaç: Bu çalışmanın amacı gastrointestinal sistemin cerrahi patolojilerine eşlik eden konjenital anomalileri değerlendirmektir.

Gereç ve Yöntem: 2015-2018 yılları arasında yenidoğan yoğun bakım ünitesine gastrointestinal sistem cerrahi patolojileri nedeniyle başvuran hastaların tıbbi kayıtları retrospektif olarak ilişkili konjenital anomaliler açısından değerlendirildi.

Bulgular: Çalışma süresince 67 hasta tespit edildi. En sık rastlanan gastrointestinal sistem patolojisi 15 olguda (% 22.4) anal atrezi, bunu 14 olguda (% 20.9) diyafragma hernisi, özofagus atrezisi (n: 10) ve ileal atrezi (n: 10) (% 14.9) izledi. Otuz iki hastada (% 48.8) gastrointestinal sistem patolojilerine eşlik eden konjenital anomali saptandı. Konjenital kalp hastalığı en sık görülen anomaliydi ve en sık birliktelik 18 olguda (% 26.8) atriyal septal defekt idi. Ek olarak, (n: 13)% 19.4'ünde kompleks konjenital kalp hastalığı vardı. On iki hastaya (% 17.9) ekstrakardiyak anomaliler eşlik etmekteydi. Üç hastada (% 4.5) hidronefroz ve safra kesesi çamuru vardı. Vezikoüreteral reflü, ektopik böbrek veya polispleni, her bir olguda ayrı bir anomali olarak tespit edildi. Olgularımızın % 54’ü prematüre olarak doğmuştu.

Sonuç: Gastrointestinal sistem patolojileri sıklıkla konjenital kalp hastalıkları gibi çoklu anomaliler ile ilişkilidir. Ek olarak, GIS patolojilerinin prematüre bebeklerde daha sık görülmesi muhtemeldir.

Anahtar Kelimeler

newborn,gastrointestinal pathologies

Evaluation of congenital anomalies accompanying to gastrointestinal system surgical pathologies

Öz

Purpose: The aim of this study was to review accompanied congenital anomalies to gastrointestinal pathologies.

Materials and Methods: The medical records of patients who were admitted to neonatal intensive care unit with gastrointestinal system surgical pathologies during 2015-2018 were retrospectively evaluated for associated congenital anomalies.

Results: 67 patients were identified during the study period. The most common gastrointestinal system pathology was anal atresia in 15 cases (22.4%), followed by diaphragmatic hernia in 14 cases (20.9%), esophageal atresia (n:10) and ileal atresia (n:10) (14.9%). Thirty two patients (48.8%) have had accompanied congenital anomalies to gastrointestinal system pathologies. Congenital heart disease was the most common anomaly and the most frequent one was atrial septal defect in 18 cases (26.8%). In addition, there was complex congenital heart disease in (n:13) 19.4%. In 12 patients (17.9%), accompanied extracardiac anomalies were detected. Hydronephrosis and sludge in gall bladder were detected in three patients (4.5%). Vesicoureteral reflux or ectopic kidney or polysplenia was detected as a separate anomaly in each case. In our cases, prematurity rate was found in 54%.

Conclusion: Gastrointestinal system pathologies are frequently associated with multiple anomalies, especially with congenital heart diseases. In addition, these patients are likely to be preterm baby.

Anahtar Kelimeler

newborn,gastrointestinal pathologies

Kaynakça

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Ayrıntılar

Birincil Dil

İngilizce

Konular

Sağlık Kurumları Yönetimi

Bölüm

Araştırma Makalesi

Yazarlar

Murat Konak ^*
0000-0001-8728-4541
Türkiye

Ahmet Sert
0000-0002-1607-7569
Türkiye

Metin Gündüz
0000-0002-6070-0135
Türkiye

Hanifi Soylu
0000-0003-0367-859X
Türkiye

Saime Sündüs Uygun Bu kişi benim
0000-0002-6694-8115
Türkiye

Yayımlanma Tarihi

30 Haziran 2019

Gönderilme Tarihi

11 Eylül 2018

Kabul Tarihi

12 Aralık 2018

Yayımlandığı Sayı

Yıl 2019 Cilt: 44 Sayı: 2

DOI

https://doi.org/10.17826/cumj.458835

IZ

https://izlik.org/JA93BY32NG

APA

Konak, M., Sert, A., Gündüz, M., Soylu, H., & Sündüs Uygun, S. (2019). Evaluation of congenital anomalies accompanying to gastrointestinal system surgical pathologies. Cukurova Medical Journal, 44(2), 425-430. https://doi.org/10.17826/cumj.458835

AMA

1.Konak M, Sert A, Gündüz M, Soylu H, Sündüs Uygun S. Evaluation of congenital anomalies accompanying to gastrointestinal system surgical pathologies. Cukurova Med J. 2019;44(2):425-430. doi:10.17826/cumj.458835

Chicago

Konak, Murat, Ahmet Sert, Metin Gündüz, Hanifi Soylu, ve Saime Sündüs Uygun. 2019. “Evaluation of congenital anomalies accompanying to gastrointestinal system surgical pathologies”. Cukurova Medical Journal 44 (2): 425-30. https://doi.org/10.17826/cumj.458835.

EndNote

Konak M, Sert A, Gündüz M, Soylu H, Sündüs Uygun S (01 Haziran 2019) Evaluation of congenital anomalies accompanying to gastrointestinal system surgical pathologies. Cukurova Medical Journal 44 2 425–430.

IEEE

[1]M. Konak, A. Sert, M. Gündüz, H. Soylu, ve S. Sündüs Uygun, “Evaluation of congenital anomalies accompanying to gastrointestinal system surgical pathologies”, Cukurova Med J, c. 44, sy 2, ss. 425–430, Haz. 2019, doi: 10.17826/cumj.458835.

ISNAD

Konak, Murat - Sert, Ahmet - Gündüz, Metin - Soylu, Hanifi - Sündüs Uygun, Saime. “Evaluation of congenital anomalies accompanying to gastrointestinal system surgical pathologies”. Cukurova Medical Journal 44/2 (01 Haziran 2019): 425-430. https://doi.org/10.17826/cumj.458835.

JAMA

1.Konak M, Sert A, Gündüz M, Soylu H, Sündüs Uygun S. Evaluation of congenital anomalies accompanying to gastrointestinal system surgical pathologies. Cukurova Med J. 2019;44:425–430.

MLA

Konak, Murat, vd. “Evaluation of congenital anomalies accompanying to gastrointestinal system surgical pathologies”. Cukurova Medical Journal, c. 44, sy 2, Haziran 2019, ss. 425-30, doi:10.17826/cumj.458835.

Vancouver

1.Murat Konak, Ahmet Sert, Metin Gündüz, Hanifi Soylu, Saime Sündüs Uygun. Evaluation of congenital anomalies accompanying to gastrointestinal system surgical pathologies. Cukurova Med J. 01 Haziran 2019;44(2):425-30. doi:10.17826/cumj.458835