Myxoid Leiomyosarcoma

Year 2013, Volume: 38 Issue: 1, 146 - 150, 01.03.2013

Carlo Pafumi Maria Cristina Teodoro Alfio D'agati İlaria Marilli Gianluca Leanza Vito Leanza

Abstract

A 37 year old woman (para 1 spontaneous delivery) was admitted to our university hospital for menometrorrhagia. The case history showed that the patient had menometrorrhagia for six months; moreover, during the abdominal examination we found a mass (fig.1) occupying the hipogastric and mesogastric area. The tumefaction was hard and it reached the level of the umbilicus. On combined vaginal-abdominal examination a mass on the anterior wall and multiple myomata were felt; the uterus was found to have been enlarged to the size equivalent to 18 weeks pregnancy; adnexa regular were felt. During the surgery multiple myomas were found.The largest,10 cm diameter, was soft in consistence with a gelatinous structure. Total abdominal hysterectomy with preservation of adnexa was performed. Histopathological result gave evidence of myxoidleiomyosarcoma in the largest myoma, whereas the others fibroid nodes were without atypia

Keywords

mixoid leiomiosarcoma, uterus, miomectomia

Miksoid Leiomyosarkoma

Abstract

Menometroraji teşhisi ile 37 yaşındaki bir bayan (doğum sayısı 1, spontan doğum) universite hastanemize kabul edildi. Vaka hikayesinde 6 ay öncesinde menometroraji ile teşhis edildiği görülen hastada abdominal incelemeler neticesinde hipogastrik ve mezogastrik bölgeleri kapsayan bir kitle tespit ettik. Tümefaksiyon sert ve umblikus seviyesine ulaşmıştı. Birleşik vajinal-abdominal incelemede anterior duvarda kitle ve multipl myeloma hissedildi; uterus 18 haftalık gebeliktekine denk bir şekilde genişlemişti; adneks normal olarak hissedildi. Cerrahi operasyonda multipl miyelomlar tespit edildi. En büyüğü 10 cm çapında jelatinli yumuşak bir yapısı vardı. Adneksin korunduğu total abdominal histerektomi gerçekleştirildi. Histopatolajik sonuçlar en büyük miyomda miksoid leiomyosarkom olduğunu gösterirken, diğer fibroid nodları atipi içermemektedir.

Keywords

Miksoid leiomyosarkom, klinik bulgular, ultrasonografi, doppler

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• Yazışma Adresi / Address for Correspondence: Dr. Carlo Pafumi Deparment of Surgery Catania Universıty ITALY e mail: [e-mail] geliş tarihi/received :10.08.2012 kabul tarihi/accepted:17.09.2012