Yıl 2012, Cilt 15 , Sayı 2, Sayfalar 149 - 155 2012-04-19

Papillon-Lefevre Syndrome: Report of two cases in the same family

Arzu YILDIRIM BİCER [1] , İlkay PEKER [2] , Oguzhan DEMİREL [3]


Papillon-Lefevre syndrome (PLS) is a rare autosomal recessive disorder characterized by the association of palmoplantar hyperkeratosis and premature loss of both deciduous and permanent  teeth. Two siblings (29-years-old female and 36-years-old male) with PLS who complained about early teeth loss, esthetic problems and difficulty during eating and speech refered to our clinic. After intraoral and radiologic examination we planned total prosthesis to first case’s upper and lower jaw and partial prosthesis to second patient’s upper and lower jaw. Patients’ financial problem affected the treatment planning. This case report presents prosthodontic rehabilitation of two patients with PLS in the same family.

Papillon Lefevre syndrome, Palmoplantar keratoderma, loss of dentition
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Birincil Dil en
Bölüm Case Reports
Yazarlar

Yazar: Arzu YILDIRIM BİCER

Yazar: İlkay PEKER

Yazar: Oguzhan DEMİREL

Tarihler

Başvuru Tarihi : 2 Nisan 2011
Kabul Tarihi : 18 Nisan 2021
Yayımlanma Tarihi : 19 Nisan 2012

EndNote %0 Cumhuriyet Dental Journal Papillon-Lefevre Syndrome: Report of two cases in the same family %A Arzu Yıldırım Bicer , İlkay Peker , Oguzhan Demirel %T Papillon-Lefevre Syndrome: Report of two cases in the same family %D 2012 %J Cumhuriyet Dental Journal %P 1302-5805-2146-2852 %V 15 %N 2 %R doi: 10.7126/cdj.2012.803 %U 10.7126/cdj.2012.803