Hereditary angioedema (HA) is a rare disorder
characterized by recurrent angioedema attacks and autosomal dominant
transmission. Plasma C1 occurs due to esterase inhibitor deficiency. Angioedema
is most commonly seen in the extremities, oropharynx, and visceral organs.
Intestinal mucosal edema can cause temporary obstruction and severe abdominal
pain that can interfere with acute abdomen. It should be kept in mind that
antihistamines, stereoids, androgens, FFP (Fresh frozen plasma) and C1 esterase
inhibitors used in the treatment of these patients may also develop allergies
and these drugs should be used with caution.
We aimed to present a 51 years old female patient (Figure-1) with a
diagnosis of hereditary angioedema in our case which developed FFP (Fresh
frozen plasma) allergy.
Birincil Dil | İngilizce |
---|---|
Konular | Yoğun Bakım |
Bölüm | Case Reports |
Yazarlar | |
Yayımlanma Tarihi | 23 Nisan 2019 |
Gönderilme Tarihi | 17 Ocak 2019 |
Kabul Tarihi | 8 Nisan 2019 |
Yayımlandığı Sayı | Yıl 2019 Cilt: 1 Sayı: 1 |