Yıl 2020, Cilt 6 , Sayı 1, Sayfalar 77 - 82 2020-01-04

Congenital adrenal hyperplasia with an ovarian adrenal rest tumor: a case report

Betül AYDIN BUYRUK [1] , Göknur YORULMAZ [2] , Ayşe Nur DEĞER [3] , Medine Nur KEBAPÇI [4]


Adrenal rest tumors (ART) are extra-adrenal findings of adrenal tissue. Testicular adrenal rest tumors (TART) are widespread in males with congenital adrenal hyperplasia (CAH). Ovarian adrenal rest tumours (OART), which form in females with CAH, are less commonly seen. Reports in literature of OART are extemely rare. The case is here presented of a 43-year-old female who was diagnosed at the age of 15 years with CAH and underwent bilateral adrenalectomy at the age of 37. On presentation at our clinic, 4×2 cm mass was determined on the right adnexa in the advanced tests and a right-side salpingo-oopherectomy was performed. The pathology examination reported heterotopic adrenal cortical tissue. Routine ovarian imaging in females with CAH is not indicated. Although OART are rarely seen, they should be kept in mind and these patients should be evaluated radiologically together with laboratory tests. 

Ovarian adrenal rest tumor, congenital adrenal hyperplasia
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Birincil Dil en
Konular Endokrinoloji ve Metabolizma
Bölüm Case Report
Yazarlar

Orcid: 0000-0003-3476-3877
Yazar: Betül AYDIN BUYRUK (Sorumlu Yazar)
Kurum: Department of Endocrinology, Osmangazi University School of Medicine, Eskişehir, Turkey
Ülke: Turkey


Orcid: 0000-0001-8596-9344
Yazar: Göknur YORULMAZ
Kurum: Department of Endocrinology, Osmangazi University School of Medicine, Eskişehir, Turkey
Ülke: Turkey


Orcid: 0000-0001-9674-0799
Yazar: Ayşe Nur DEĞER
Kurum: Department of Endocrinology, Dumlupınar University, Kütahya Evliya Çelebi Training and Research Hospital, Kütahya, Turkey
Ülke: Turkey


Orcid: 0000-0002-8286-5256
Yazar: Medine Nur KEBAPÇI
Kurum: Department of Endocrinology, Osmangazi University School of Medicine, Eskişehir, Turkey
Ülke: Turkey


Tarihler

Yayımlanma Tarihi : 4 Ocak 2020

EndNote %0 The European Research Journal Congenital adrenal hyperplasia with an ovarian adrenal rest tumor: a case report %A Betül AYDIN BUYRUK , Göknur YORULMAZ , Ayşe Nur DEĞER , Medine Nur KEBAPÇI %T Congenital adrenal hyperplasia with an ovarian adrenal rest tumor: a case report %D 2020 %J The European Research Journal %P -2149-3189 %V 6 %N 1 %R doi: 10.18621/eurj.435638 %U 10.18621/eurj.435638