Three cases with Klippel-Trenaunay syndrome and treatment options

Year 2020, Volume: 6 Issue: 2, 169 - 172, 04.03.2020

Ersin Çelik , İlker Alat

https://doi.org/10.18621/eurj.480577

Abstract

Klippel-Trenaunay syndrome (KTS) is a rare congenital anomaly
characterized by capillary malformations, soft tissue and bone hypertrophy and
varicosities. The presence of at least two of the three clinical conditions is
sufficient for the diagnosis of KTS. Early diagnosis and treatment are important
because of possible serious complications such as deep vein thrombosis and
pulmonary embolism. Venous system aplasia and/or hypoplasia might be observed
in KTS. Therefore, deep venous system must be evaluated definitely before
determining the treatment strategy. It's herein presented our conservative and
surgical treatment applications in three KTS patients. 

Keywords

Klippel-Trenaunay syndrome, embryonic, varicose, venous, venous insufficiency, stripping

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