Lesions and Complications Associated with Bicuspid Aortic Valve

Abstract

Bicuspid aortic valve (BAV) is the most common congenital cardiovascular malformation. Its incidence is 0,5-2% in the whole population. It is 3 times more common in boys than girls. Bicuspid aortic valve can be defined as the aortic valve having two leaflets instead of three. The prevalence of patients with bicuspid aortic valve in first degree family relatives is 10% and familial transmission has been reported. BAV is a clinically important condition as it accompanies serious potential complications including aortic valve dysfunction, infective endocarditis, aortic dilation, aortic aneurysm, and aortic dissection. By identifying individuals with BAV, important complications that may develop can be prevented and the timing of the interventions that can be performed can be decided. In this review, the definition of BAV, its clinical importance and the most common accompanying complications were presented.

Keywords

• bicuspid aortic valve
• echocardiography
• congenital valve disease

Biküspid Aort Kapağı İle İlişkili Lezyonlar ve Komplikasyonlar

Abstract

Biküspid aort kapağı (BAK) en sık görülen doğumsal kardiyovasküler malformasyondur. Görülme sıklığı tüm popülasyonda %0,5-2’dir. Erkeklerde kızlardan 3 kat daha fazla görülür. Biküspit aort kapağı, aort kapağının üç yaprakçık yerine iki yaprakçık yapısına sahip olması olarak tanımlanabilir. Biküspit aort kapağı olan hastaların 1.derece aile yakınlarında görülme sıklığı %10 olup ailesel geçiş bildirilmiştir. Aort kapak işlev bozukluğu, infektif endokardit, aort genişlemesi, aort anevrizması ve aort diseksiyonunu içeren ciddi potansiyel komplikasyonlara eşlik ettiğinden BAK klinik olarak önemli bir durumdur. BAK olan bireylerin tespit edilmesi ile gelişebilecek olan önemli komplikasyonlar önlenebilir ve yapılabilecek olan girişimlerin zamanlamasına karar verilebilir. Bu derlemede BAK’ın tanımı, klinik olarak önemi ve en sık eşlik eden komplikasyonları sunulmuştur.

Keywords

• Biküspid aort kapağı
• ekokardiyografi
• konjenital kalp hastalığı

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