Intraabdominal Synovial Sarcoma, A Rare Tumour and Rare Localisation

Yıl 2018, , 669 - 673, 30.09.2018

Mustafa Yener Uzunoğlu , Fatih Altıntoprak , Enis Dikicier , Zeynep Kahyaoğlu

https://doi.org/10.31832/smj.404264

Öz

Synovial
sarcomas are often seen in the soft tissues, intra-abdominal synovial sarcomas
are extremely rare. An intra-abdominal mass starting from the umbilicus and
extending into the pelvis was detected in a 53-year-old man admitted with
abdominal pain and a palpable mass. Total mass excision surgery was performed
and the mass was found to be an intra-abdominal synovial sarcoma arise from
small bowel wall histopathologically. Unfortunately, this is a malignancy with
a poor prognosis and a short survival despite all therapeutic efforts

Anahtar Kelimeler

intra-abdominal mass, sarcoma, small bowel wall

Intraabdominal Sinovyal Sarkom, Nadir Lokalizasyonda Nadir Bir Tümör

Öz

Sinovyal
sarkomlar sıklıkla yumuşak dokuda gözlenirler, intra abdominal sinovyal
sarkomlar oldukça nadirdir. Karın ağrısı ve palpabl kitle ile başvuran 53 yaşında
erkek bir hastada umbilikustan başlayıp, pelvise kadar uzanım gösteren karın içi
kitle saptandı. Total kitle eksizyonu yapılan hastada, histopatolojik olarak
ince barsak duvarından kaynaklanan intraabdominal sinovyal sarkom bulundu. Ne
yazık ki, bu malignite zayıf prognoza sahiptir ve yapılan tüm tedavilere rağmen
sağkalımı kısadır.

Anahtar Kelimeler

ince barsak duvarı, intraabdominal kitle, sarkom

Kaynakça

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