Intraabdominal Synovial Sarcoma, A Rare Tumour and Rare Localisation

Abstract

Synovial sarcomas are often seen in the soft tissues, intra-abdominal synovial sarcomas are extremely rare. An intra-abdominal mass starting from the umbilicus and extending into the pelvis was detected in a 53-year-old man admitted with abdominal pain and a palpable mass. Total mass excision surgery was performed and the mass was found to be an intra-abdominal synovial sarcoma arise from small bowel wall histopathologically. Unfortunately, this is a malignancy with a poor prognosis and a short survival despite all therapeutic efforts

Keywords

• intra-abdominal mass,sarcoma,small bowel wall

Intraabdominal Sinovyal Sarkom, Nadir Lokalizasyonda Nadir Bir Tümör

Abstract

Sinovyal sarkomlar sıklıkla yumuşak dokuda gözlenirler, intra abdominal sinovyal sarkomlar oldukça nadirdir. Karın ağrısı ve palpabl kitle ile başvuran 53 yaşında erkek bir hastada umbilikustan başlayıp, pelvise kadar uzanım gösteren karın içi kitle saptandı. Total kitle eksizyonu yapılan hastada, histopatolojik olarak ince barsak duvarından kaynaklanan intraabdominal sinovyal sarkom bulundu. Ne yazık ki, bu malignite zayıf prognoza sahiptir ve yapılan tüm tedavilere rağmen sağkalımı kısadır.

Keywords

• ince barsak duvarı,intraabdominal kitle,sarkom

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