Prenatal ve Postnatal Dönemde Tanı Alan Konjenital Akciğer Malformasyonu Olan Çocukların Değerlendirilmesi

Yıl 2022, Cilt: 16 Sayı: 4, 336 - 342, 07.07.2022

Tuğba Ramaslı Gürsoy Tuğba Şişmanlar Eyüboğlu , Ayşe Tana Aslan , Ramazan Karabulut , Abdullah Taştepe

https://doi.org/10.12956/tchd.1034487

Öz

Amaç: Çalışmamızda prenatal ve postnatal dönemde tanı alan konjenital akciğer malformasyonu olan hastaların klinik özelliklerini
karşılaştırmayı amaçladık.

Gereç ve Yöntemler: 2007-2021 yılları arasında Çocuk Göğüs Hastalıkları Bölümü’nde izlenen konjenital akciğer malformasyonu olan
hastalar cinsiyetleri, yaşları, başvuru yakınmaları, ilk semptom zamanı, tanı yaşları, tanı yöntemleri, doğum haftaları, doğum ağırlıkları,
ebeveyn akrabalığı, operasyon varlığı, operasyon yaşı ve endikasyonları, uzun dönem komplikasyonları açısından değerlendirildi. Prenatal
dönemde tanı alan hastalar ile postnatal dönemde tanı alanlar klinik özellikleri açısından karşılaştırıldı.

Bulgular: Konjenital akciğer malformasyonu nedeniyle izlenen 37 hastanın ortalama yaşları 6.7±5.8 yıldı ve 17’si (%45.9) kızdı. Prenatal
dönemde tanı alan hastalar (n:18) yakınması olmadan başvururken diğer hastaların en sık başvuru nedenleri öksürük ve tekrarlayan akciğer
enfeksiyonuydu. Postnatal dönemde tanı alan hastaların (n:19) ortanca tanı yaşları 30 (en küçük:10; en büyük:1080) gündü. Hastaların
18’i (%48.6) prenatal ultrasonografi, 14’ü (%37.8) bilgisayarlı tomografi, beşi (%13.6) akciğer grafisi ile tanı aldı. İzlemde iki hastanın
malformasyonu kendiliğinden geriledi. Oniki hasta opere olurken diğer hastalar mevcut anomalileri ile takip edilmektedir. Prenatal dönemde
tanı alan hastaların asemptomatik izlem süresi, postnatal tanı alan hastalardan istatistiksel olarak anlamlı farklıydı (36.5±4.7 ve 24.0±12.7
ay) (p:0.004).

Sonuç: Çalışmamızda prenatal dönemde tanı alan konjenital akciğer malformasyonu olan hastaların daha uzun süre

Anahtar Kelimeler

Çocuk, konjenital akciğer malformasyonu, prenatal tanı

Evaluation of Children with Congenital Lung Malformations Who Were Diagnosed in The Prenatal and Postnatal Period

Öz

Objective: We aimed to compare clinical features of children with congenital lung malformations (CLM) who were
diagnosed in prenatal and postnatal period.

Material and Methods: Children with CLM followed in our pediatric pulmonology department between 2007-2021
were evaluated in terms of sex, age, complaints at presentation, time of onset of symptoms, age at diagnosis, diagnostic
methods, gestational ages, birth weights, parental consanguinity, presence of any operations, age and indications of
operations and long-term complications. Children who were diagnosed in prenatal period and those in postnatal period
were compared in terms of their clinical features.

Results: The mean age of 37 children with CLM was 6.7±5.8 years, and seventeen (45.9%) of the children were girls.
Children who were diagnosed during the prenatal period (n:18) had no complaints, whereas cough and recurrent
pneumonia were the most common reasons at admission in others. Median age at diagnosis of children who
were postnatally diagnosed (n:19) was 30 days (10-1080). Eighteen (48.6%) children were diagnosed by prenatal
ultrasonography, 14 (37.8%) by computed tomography, and five (13.6%) by chest X-ray. During follow-up, malformations
of two children regressed spontaneously. Twelve children were operated while others were followed up with their
anomalies. Asymptomatic follow-up duration of children who were prenatally diagnosed was significantly different than
the children who were diagnosed in the postnatal period (36.5±4.7 vs 24.0±12.7 months) (p:0.004).

Conclusion: Children with CLM who were diagnosed in the prenatal period were found to remain asymptomatic for
longer. Prenatal diagnosis enables them to live longer without symptoms with appropriate surgical timing.

Anahtar Kelimeler

Child, congenital lung malformations, prenatal diagnosis

Kaynakça

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