Marginal zone lymphoma presenting in a patient with autoimmune hemolytic anemia: a case report

Year 2022, Volume: 4 Issue: 2, 80 - 82, 29.04.2022

Büşra Güner , Bedrettin Orhan , Tuba Ersal , Vildan Ozkocaman , Rıdvan Ali , Fahir Özkalemkaş

https://doi.org/10.46310/tjim.904114

Abstract

While autoimmune hemolytic anemia (AIHA) is expected in non-Hodgkin’s lymphomas, it is less common in marginal zone lymphoma. Sixty-year-old male patient was followed up with hemolytic anemia in our clinic and while the etiology was investigated, scattered nodes in the mediastinum and abdomen compatible with lymphoproliferative disease were observed on CT, and positive detection of CD5, CD19, CD20, CD22, CD45, HLA-DR, FMC-7 on flow cytometry sent from peripheral blood and a diagnosis of low grade B cell lymphoma (MZL) was made with the result of bone marrow pathology. We found it appropriate to present our MZL case because of its response to steroid treatment and its rare presentation with AIHA.

Keywords

AUTOIMMUNE HEMOLITHIC ANEMIA, MARGINAL ZONE LYMPHOMA, LYMPHOMA

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