RUSSELL-SILVER SYNDROME: A CASE REPORT

Gülşah Balan

RUSSELL-SILVER SYNDROME: A CASE REPORT

Abstract

In 1953 and 1954, Silver and Russell independently described groups of small children whose pregnancies had complicated by intrauterine growth retardation with a both genetically and clinically heterogeneous disorder named Russel Silver Syndrome [RSS/SRS; OMIM 180860]. This case report describes the dental complications of the syndrome. A 4-yearold girl diagnosed with RSS at the Medical Faculty Hospital of Marmara University was directed to Marmara University Department of Pediatric Dentistry for dental examination. Severe dentin caries and pulpitis were detected in many teeth of the primary dentition as an indication of the child being in the high caries risk group (dft/dfs = 13/37). RSS-diagnosed children first experience nutritional difficulty and later face severe dental caries as a consequence.

Keywords

russel Silver Syndrome,hypoglicemia

References

[1] Silver HK, Kiyasu W, George J, Deamer WC. Syndrome of congenital hemihypertrophy, shortness of stature, and elevated urinary gonadotropins. Pediatrics. 1953;12(4):368-76.
[2] Russell A. A syndrome of intra-uterine dwarfism recognizable at birth with craniofacial dysostosis, disproportionately short arms, and other anomalies (5 examples). Proc R Soc Med. 1954;47(12):1040-4.
[3] Binder G, Begemann M, Eggermann T, Kannenberg K. Silver-Russell syndrome. Best Pract Res Clin Endocrinol Metab. 2011;25(1):153-60.
[4] Price S, Stanhope R, Garrett C, Preece M, Trembath R. The spectrum of SilverRussell syndrome: a clinical and molecular genetic study and new diagnostic criteria. Journal of medical genetics. 1999;36(11):83742.
[5] Hansen KK, Latson LA, Buehler BA, Latson LA. Silver-Russell syndrome with unusual findings. Pediatrics. 1987;79(1):1258.
[6] Wee SA. Russell-Silver syndrome. Dermatology online journal. 2007;13(1):16.
[7] Blissett J, Harris G, Kirk J. Feeding problems in Silver-Russell syndrome. Developmental Medicine & Child Neurology. 2001;43(1):39-44.
[8] Sato C, Ogawa T, Tsuge R, Shiga M, Tsuji M, Baba Y, et al. Systemic and maxillofacial characteristics of 11 Japanese children with Russell-Silver syndrome. Congenit Anom (Kyoto). 2016;56(5):217-25.

Details

Primary Language

English

Subjects

Health Care Administration

Journal Section

Research Article

Authors

Gülşah Balan This is me

Publication Date

October 2, 2017

Submission Date

August 10, 2017

Acceptance Date

-

Published in Issue

Year 2017 Volume: 3 Number: 2

IZ

https://izlik.org/JA55AD49SC

Cite

RIS / Bibtex

APA

Balan, G. (2017). RUSSELL-SILVER SYNDROME: A CASE REPORT. Aydın Dental Journal, 3(2), 31-36. https://izlik.org/JA55AD49SC

AMA

1.Balan G. RUSSELL-SILVER SYNDROME: A CASE REPORT. Aydin Dental Journal. 2017;3(2):31-36. https://izlik.org/JA55AD49SC

Chicago

Balan, Gülşah. 2017. “RUSSELL-SILVER SYNDROME: A CASE REPORT”. Aydın Dental Journal 3 (2): 31-36. https://izlik.org/JA55AD49SC.

EndNote

Balan G (October 1, 2017) RUSSELL-SILVER SYNDROME: A CASE REPORT. Aydın Dental Journal 3 2 31–36.

IEEE

[1]G. Balan, “RUSSELL-SILVER SYNDROME: A CASE REPORT”, Aydin Dental Journal, vol. 3, no. 2, pp. 31–36, Oct. 2017, [Online]. Available: https://izlik.org/JA55AD49SC

ISNAD

Balan, Gülşah. “RUSSELL-SILVER SYNDROME: A CASE REPORT”. Aydın Dental Journal 3/2 (October 1, 2017): 31-36. https://izlik.org/JA55AD49SC.

JAMA

1.Balan G. RUSSELL-SILVER SYNDROME: A CASE REPORT. Aydin Dental Journal. 2017;3:31–36.

MLA

Balan, Gülşah. “RUSSELL-SILVER SYNDROME: A CASE REPORT”. Aydın Dental Journal, vol. 3, no. 2, Oct. 2017, pp. 31-36, https://izlik.org/JA55AD49SC.

Vancouver

1.Gülşah Balan. RUSSELL-SILVER SYNDROME: A CASE REPORT. Aydin Dental Journal [Internet]. 2017 Oct. 1;3(2):31-6. Available from: https://izlik.org/JA55AD49SC