RUSSELL-SILVER SYNDROME: A CASE REPORT
Öz
In 1953 and 1954, Silver and Russell independently described groups of small children whose pregnancies had complicated by intrauterine growth retardation with a both genetically and clinically heterogeneous disorder named Russel Silver Syndrome [RSS/SRS; OMIM 180860]. This case report describes the dental complications of the syndrome. A 4-yearold girl diagnosed with RSS at the Medical Faculty Hospital of Marmara University was directed to Marmara University Department of Pediatric Dentistry for dental examination. Severe dentin caries and pulpitis were detected in many teeth of the primary dentition as an indication of the child being in the high caries risk group (dft/dfs = 13/37). RSS-diagnosed children first experience nutritional difficulty and later face severe dental caries as a consequence.
Anahtar Kelimeler
Kaynakça
- [1] Silver HK, Kiyasu W, George J, Deamer WC. Syndrome of congenital hemihypertrophy, shortness of stature, and elevated urinary gonadotropins. Pediatrics. 1953;12(4):368-76.
- [2] Russell A. A syndrome of intra-uterine dwarfism recognizable at birth with craniofacial dysostosis, disproportionately short arms, and other anomalies (5 examples). Proc R Soc Med. 1954;47(12):1040-4.
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- [8] Sato C, Ogawa T, Tsuge R, Shiga M, Tsuji M, Baba Y, et al. Systemic and maxillofacial characteristics of 11 Japanese children with Russell-Silver syndrome. Congenit Anom (Kyoto). 2016;56(5):217-25.
Ayrıntılar
Birincil Dil
İngilizce
Konular
Sağlık Kurumları Yönetimi
Bölüm
Araştırma Makalesi
Yazarlar
Gülşah Balan
Bu kişi benim
Yayımlanma Tarihi
2 Ekim 2017
Gönderilme Tarihi
10 Ağustos 2017
Kabul Tarihi
-
Yayımlandığı Sayı
Yıl 2017 Cilt: 3 Sayı: 2