The combination of idiopathic pulmonary hemosiderosis and celiac disease: Case report

Yıl 2007, Cilt: 6 Sayı: 1, 37 - 40, 01.04.2007

Ahmet Erdil Yüksel Ateş Kemalettin Yılmaz Önder Öngürü Deniz Doğan Kemal Dağalp

Öz

Idiopathic pulmonary hemosiderosis is a rare disease of unknown etiology usually characterized by recurrent episodes of alveolar hemorrhage, hemoptysis and iron deficiency anemia. It occurs most frequently in children but rarely in adults. The combination of idiopathic pulmonary hemosiderosis and celiac disease is also extremely rare. A 21-year-old man with history of recurrent hemoptysis and anemia was diagnosed with the combination of idiopathic pulmonary hemosiderosis and celiac disease. The patient was started on a gluten-free diet and has had no recurrences of hemoptysis over 6 months' follow-up. Hemoglobin at 6 months' follow up was 13.4 g/dL, while antiendomysial antibody titers had declined to 63,204 IU/ml.

Anahtar Kelimeler

Idiopathic pulmonary hemosiderosis, celiac disease

İdiopatik pulmoner hemosiderozis ile çölyak hastalığı birlikteliği: Olgu sunumu

Öz

İdiopatik pulmoner hemosiderosis tekrarlayan alveolar hemoraji, hemoptizi ve demir eksikliği anemisi ile birlikte seyreden ve nedeni bilinmeyen nadir bir hastalıktır. Hastalık genellikle çocuklarda bulunmasına rağmen, seyrekte olsa erişkinlerde de tespit edilebilmektedir. İdiopatik pulmoner hemosiderosis ile çölyak hastalığının birlikte bulunması da oldukça seyrek görülen bir durumdur. Bu vakada derin anemi ve tekrarlayan hemoptizileri olan 21 yaşındaki bir erkek hastada idiopatik pulmoner hemosiderosis ile birlikte çölyak hastalığı birlikteliği tespit edildi. Hastaya glutensiz diyet verildikten 6 ay sonraki kontrolünde hemoptizisi düzelmişti. Altı ayın sonunda hemoglobini 13.4 g/dl'ye yükseldi ve anti-endomisyal antikor seviyeleri 63,204 IU/ml'ye geriledi.

Anahtar Kelimeler

İdiopatik pulmoner hemosiderosis, çölyak hastalığı

Kaynakça

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