Sigara İçmesine Rağmen Oniki Yılda Progresyon Göstermeyen Pulmoner Langerhans Hücreli Histiyositoz Olgusu

Abstract

Pulmoner langerhans hücreli histiositozis PLHH X; langerhans hücreli histiyositozisin alt grubu olup akciğerlerde langerhans hücre infiltrasyonunun görüldüğü, nedeni bilinmeyen nadir bir interstisyel akciğer hastalığıdır. PLHH prevalansı ile ilgili kesin bir veri yoktur. Bazı çalışmalarda prevalansı erkekler ve kadınlar için sırasıyla 0,27/100 000 ve 0,07/100 000 olarak tespit edilmiştir. Olguların büyük bir kısmının sigara içicisi olması patogenezinde sigaranın önemli bir yer tuttuğunu düşündürmektedir. Sigara içmesine rağmen 12 yılda progresyon göstermeyen nadir bir olguyu literatür eşliğinde sunuyoruz

Keywords

• Erişkin, Histiyositoz, Pulmoner langerhans hücreli, Radyoloji

Pulmonary Langerhans Cell Histiocytosis Case that not Shows any Progress although Smoking

Abstract

Pulmonary Langerhans Cell Histiocytosis PLCH X, which is a subgroup of Langerhans Cell Histiocytosis, is an idiopathic interstitial lung disease in which Langerhans cell infiltration is seen in the lung. There is no certain data on the prevalence of PLHH. In some studies, the estimated prevalence was calculated as 0.27 and 0.07 per 100000 population in males and females respectively. Due to the large number of cases that are smokers, it is considered that the pathogenesis is related to smoking. We are presenting a rare case that has not progressed for 12 years despite smoking

Keywords

• Adult, Histiocytosis, Pulmonary Langerhans cell, Radiology

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