Maksillofasiyal Belirtileriyle Sistemik Sklerozis: Olgu Sunumu

Öz

Sistemik sklerozis nadir görülen otoimmün inflamatuvar bir hastalıktır. Sistemik skleroziste ana bulgu cildin kalınlaşması ve gerilmiş olmasıdır. Deri bulgularının yanı sıra akciğerler, böbrekler, kalp ve sindirim sistemi gibi vücudun birçok yerinde inflamasyon ve skar gelişimi izlenir. Bununla birlikte sistemik skleroz; ciltte sertleşme, ince çizgiler, derin kırışıklıklar, kserostomi, dilde sertlik ve mikrostomi sebebiyle oral ve fasiyal dokuları da ilgilendiren bir hastalıktır. Hastalığın oral bulguları, dokulardaki veya sinir ve damarlar etrafındaki kollajen birikiminden kaynaklanır ve tüm oral dokular etkilenir. En sık görülen oral bulgu, genişlemiş periodontal ligament alanlarıdır. Çalışmanın amacı sistemik sklerozu olan 46 yaşında erkek hastanın oral bulgularını sunmak ve tartışmaktır. Klinik ve radyolojik olarak oral ve fasiyal muayene yapıldı. Bu çalışmada yer alan hastanın oral semptomları; disfaji, periodontal problemler ve sınırlı ağız açıklığı idi. Sistemik sklerozis hastaları, diğer oral ve maksillofasiyal bulgular için yıllık panoramik radyografilerle düzenli izlem yaptırmalıdırlar

Anahtar Kelimeler

• Sistemik sklerozis, Oral belirtiler, Radyogram

Maxillofacial Manifestations of Systemic Sclerosis: Case Report

Abstract

Systemic Sclerosis is a rarely seen autoimmune inflammatory disease. The main sign of systemic sclerosis is a combination of thickened and stretched skin. Alongside the symptoms in the skin, inflammation and scar formation are observed in many parts of the body such as lungs, kidneys, heart, the intestinal tract. Systemic sclerosis is a disorder affecting oral and facial tissues with skin hardening, thin lips, deep wrinkles, xerostomia, tongue rigidity, and microstomia. The oral manifestations of the illness are caused by deposits of collagen in the tissues or as a result of collagen deposition around nerves and vessels, and all the oral tissues are affected. The most commonly known oral manifestation is widened periodontal ligament spaces. The aim of this study was to present and discuss the oral findings of a 46-year-old male patient with systemic sclerosis. Oral and facial examinations were performed clinically and radiologically. Results: In this study, the oral symptoms of the patient were dysphagia, periodontal problems and mouth opening limitation. SSc patients should have regular follow-up with a yearly panoramic radiograph for other oral and maxillofacial manifestations

Keywords

• Systemic sclerosis, Oral manifestations, Radiogram

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