Perikardiyal Efüzyonu Olan Proteus Sendromlu Bir Hastada Anestezi Uygulaması

Year 2021, Volume: 7 Issue: 1, 168 - 172, 01.01.2021

Emel Gündüz Hakan Keskin Tülin Aydoğdu Titiz

Abstract

Proteus syndrome PS is a rare congenital disease described by Cohen and Hayden, which is characterized by asymmetric and excess tissue growth in the body 1 . Various pathologies such as progressive skeletal deformities, tumors, vascular malformations, bullous pulmonary disease and skin lesions can be seen in these cases. There is a limited number of studies examining cardiac involvement

Keywords

Proteus syndrome, Pericardial effusion, Right double-lumen tube

Anesthesia Application in A Proteus Syndrome Patient With Pericardial Effusion

Abstract

Proteus sendromu PS , Cohen ve Hayden tarafından tanımlanan ve vücutta asimetrik ve aşırı doku büyümesi ile karakterize nadir görülen konjenital bir hastalıktır 1 . Bu olgularda ilerleyici iskelet deformiteleri, tümörler, vasküler malformasyonlar, büllöz akciğer hastalığı ve deri lezyonları gibi farklı patolojiler görülebilir. Kardiyak tutulumu inceleyen sınırlı sayıda çalışma vardır

Keywords

Proteus sendromu, Perikardiyal efüzyon, Sağ çift lümenli tüp

References

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