TR
EN
Proximal realignment surgery for unilateral chronic patella dislocation in Morquio syndrome: a case report
Abstract
Mucopolysaccharidosis IVA (MPS IVA: Morquio A syndrome) is a lysosomal storage disorder caused by a deficiency of N-acetylgalactosamine-6-sulfate sulfatase. Patients with MPS IVA appear healthy at birth. Morquio-specific radiographic changes can be observed prior to clinical signs and symptoms. Patients are usually affected by a severe joint degeneration from the 2nd or 3rd decade. Hyperlaxity of the joints is prominent due to the excess of intermediate metabolites. We report a patient with inherited dwarfism, in which a proximal soft tissue realignment procedure was performed to treat chronic patellar dislocation.
Keywords
Details
Primary Language
English
Subjects
Health Care Administration
Journal Section
Research Article
Publication Date
January 19, 2012
Submission Date
March 7, 2014
Acceptance Date
-
Published in Issue
Year 2011 Volume: 45 Number: 6
APA
Baz, A., Akalin, S., Arik, H., & Ergun, A. (2012). Proximal realignment surgery for unilateral chronic patella dislocation in Morquio syndrome: a case report. Acta Orthopaedica et Traumatologica Turcica, 45(6), 466-469. https://izlik.org/JA25JT99XZ
AMA
1.Baz A, Akalin S, Arik H, Ergun A. Proximal realignment surgery for unilateral chronic patella dislocation in Morquio syndrome: a case report. Acta Orthopaedica et Traumatologica Turcica. 2012;45(6):466-469. https://izlik.org/JA25JT99XZ
Chicago
Baz, Ali, Serdar Akalin, Hasan Arik, and Ali Ergun. 2012. “Proximal Realignment Surgery for Unilateral Chronic Patella Dislocation in Morquio Syndrome: A Case Report”. Acta Orthopaedica et Traumatologica Turcica 45 (6): 466-69. https://izlik.org/JA25JT99XZ.
EndNote
Baz A, Akalin S, Arik H, Ergun A (January 1, 2012) Proximal realignment surgery for unilateral chronic patella dislocation in Morquio syndrome: a case report. Acta Orthopaedica et Traumatologica Turcica 45 6 466–469.
IEEE
[1]A. Baz, S. Akalin, H. Arik, and A. Ergun, “Proximal realignment surgery for unilateral chronic patella dislocation in Morquio syndrome: a case report”, Acta Orthopaedica et Traumatologica Turcica, vol. 45, no. 6, pp. 466–469, Jan. 2012, [Online]. Available: https://izlik.org/JA25JT99XZ
ISNAD
Baz, Ali - Akalin, Serdar - Arik, Hasan - Ergun, Ali. “Proximal Realignment Surgery for Unilateral Chronic Patella Dislocation in Morquio Syndrome: A Case Report”. Acta Orthopaedica et Traumatologica Turcica 45/6 (January 1, 2012): 466-469. https://izlik.org/JA25JT99XZ.
JAMA
1.Baz A, Akalin S, Arik H, Ergun A. Proximal realignment surgery for unilateral chronic patella dislocation in Morquio syndrome: a case report. Acta Orthopaedica et Traumatologica Turcica. 2012;45:466–469.
MLA
Baz, Ali, et al. “Proximal Realignment Surgery for Unilateral Chronic Patella Dislocation in Morquio Syndrome: A Case Report”. Acta Orthopaedica et Traumatologica Turcica, vol. 45, no. 6, Jan. 2012, pp. 466-9, https://izlik.org/JA25JT99XZ.
Vancouver
1.Ali Baz, Serdar Akalin, Hasan Arik, Ali Ergun. Proximal realignment surgery for unilateral chronic patella dislocation in Morquio syndrome: a case report. Acta Orthopaedica et Traumatologica Turcica [Internet]. 2012 Jan. 1;45(6):466-9. Available from: https://izlik.org/JA25JT99XZ