Araştırma Makalesi

Proximal realignment surgery for unilateral chronic patella dislocation in Morquio syndrome: a case report

Cilt: 45 Sayı: 6 19 Ocak 2012
  • Ali Baz
  • Serdar Akalin
  • Hasan Arik
  • Ali Ergun
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Proximal realignment surgery for unilateral chronic patella dislocation in Morquio syndrome: a case report

Abstract

Mucopolysaccharidosis IVA (MPS IVA: Morquio A syndrome) is a lysosomal storage disorder caused by a deficiency of N-acetylgalactosamine-6-sulfate sulfatase. Patients with MPS IVA appear healthy at birth. Morquio-specific radiographic changes can be observed prior to clinical signs and symptoms. Patients are usually affected by a severe joint degeneration from the 2nd or 3rd decade. Hyperlaxity of the joints is prominent due to the excess of intermediate metabolites. We report a patient with inherited dwarfism, in which a proximal soft tissue realignment procedure was performed to treat chronic patellar dislocation.

Keywords

Ayrıntılar

Birincil Dil

İngilizce

Konular

Sağlık Kurumları Yönetimi

Bölüm

Araştırma Makalesi

Yazarlar

Serdar Akalin Bu kişi benim

Hasan Arik Bu kişi benim

Yayımlanma Tarihi

19 Ocak 2012

Gönderilme Tarihi

7 Mart 2014

Kabul Tarihi

-

Yayımlandığı Sayı

Yıl 2011 Cilt: 45 Sayı: 6

Kaynak Göster

APA
Baz, A., Akalin, S., Arik, H., & Ergun, A. (2012). Proximal realignment surgery for unilateral chronic patella dislocation in Morquio syndrome: a case report. Acta Orthopaedica et Traumatologica Turcica, 45(6), 466-469. https://izlik.org/JA25JT99XZ
AMA
1.Baz A, Akalin S, Arik H, Ergun A. Proximal realignment surgery for unilateral chronic patella dislocation in Morquio syndrome: a case report. Acta Orthopaedica et Traumatologica Turcica. 2012;45(6):466-469. https://izlik.org/JA25JT99XZ
Chicago
Baz, Ali, Serdar Akalin, Hasan Arik, ve Ali Ergun. 2012. “Proximal realignment surgery for unilateral chronic patella dislocation in Morquio syndrome: a case report”. Acta Orthopaedica et Traumatologica Turcica 45 (6): 466-69. https://izlik.org/JA25JT99XZ.
EndNote
Baz A, Akalin S, Arik H, Ergun A (01 Ocak 2012) Proximal realignment surgery for unilateral chronic patella dislocation in Morquio syndrome: a case report. Acta Orthopaedica et Traumatologica Turcica 45 6 466–469.
IEEE
[1]A. Baz, S. Akalin, H. Arik, ve A. Ergun, “Proximal realignment surgery for unilateral chronic patella dislocation in Morquio syndrome: a case report”, Acta Orthopaedica et Traumatologica Turcica, c. 45, sy 6, ss. 466–469, Oca. 2012, [çevrimiçi]. Erişim adresi: https://izlik.org/JA25JT99XZ
ISNAD
Baz, Ali - Akalin, Serdar - Arik, Hasan - Ergun, Ali. “Proximal realignment surgery for unilateral chronic patella dislocation in Morquio syndrome: a case report”. Acta Orthopaedica et Traumatologica Turcica 45/6 (01 Ocak 2012): 466-469. https://izlik.org/JA25JT99XZ.
JAMA
1.Baz A, Akalin S, Arik H, Ergun A. Proximal realignment surgery for unilateral chronic patella dislocation in Morquio syndrome: a case report. Acta Orthopaedica et Traumatologica Turcica. 2012;45:466–469.
MLA
Baz, Ali, vd. “Proximal realignment surgery for unilateral chronic patella dislocation in Morquio syndrome: a case report”. Acta Orthopaedica et Traumatologica Turcica, c. 45, sy 6, Ocak 2012, ss. 466-9, https://izlik.org/JA25JT99XZ.
Vancouver
1.Ali Baz, Serdar Akalin, Hasan Arik, Ali Ergun. Proximal realignment surgery for unilateral chronic patella dislocation in Morquio syndrome: a case report. Acta Orthopaedica et Traumatologica Turcica [Internet]. 01 Ocak 2012;45(6):466-9. Erişim adresi: https://izlik.org/JA25JT99XZ