STURGE-WEBER SYNDROME:A CASE REPORT

Year 2015, Supplement 10, 1 - 5, 21.05.2015

İbrahim Bayrakdar Fatma Çağlayan Osman Bilge

https://doi.org/10.17567/dfd.88088

Abstract

Sturge–Weber Syndrome is rare, nonhereditary, congenital neurocutaneous disease. Leptomeningeal hemanjiom, generally unilateral port wine nevus distributing trigeminal nerve region, ocular abnormally (glaucoma) are some parts of this syndrome. The present paper reports oral findings of a 18 years old female patient with Sturge-Weber Syndrome. Sturge-Weber Syndrome must be taken into account by dentists because of its various oral manifestations

Keywords

Sturge Weber Syndrome, dentistry

STURGE-WEBER SENDROMU:BİR OLGU SUNUMU

Abstract

Sturge-Weber Sendromu nadir görülen, herediter olmayan, konjenital gelişen, nörokutanöz bir hastalıktır. Bu hastalıkta leptomeningeal hemanjiom, trigeminal sinir bölgesine dağılmış genellikle tek taraflı Porto şarabı nevus, oküler anormali (glokom) görülür. Bu vaka raporunda 18 yaşındaki Sturge-Weber sendromlu bayan bir hastanın oral bulguları sunulmuştur. Sturge-Weber sendromu, hastanın sistemik durumunu etkileyebilecek çeşitli oral bulgular göstermesi sebebiyle diş hekimleri tarafından değerlendirilmesi gereken bir hastalıkdır.

Keywords

Sturge-Weber Sendromu, diş hekimliği

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